{"code":"D70.0","type":"code","title":"Congenital agranulocytosis","codeAlso":[", if applicable, mucositis (J34.81, K12.3-, K92.81, N76.81)"],"includes":["agranulocytosis","decreased absolute neurophile count (ANC)"],"modern_v":"official26","codeFirst":[],"excludes1":["neutropenic splenomegaly (D73.81)","transient neonatal neutropenia (P61.5)"],"excludes2":[],"isBillable":true,"inclusionTerms":["Congenital neutropenia","Infantile genetic agranulocytosis","Kostmann's disease"],"useAdditionalCode":["code for any associated:","fever (R50.81)"],"clinicalDefinition":"Congenital agranulocytosis is a billable ICD-10-CM diagnosis code (D70.0). Includes: agranulocytosis; decreased absolute neurophile count (ANC). Inclusion terms: Congenital neutropenia; Infantile genetic agranulocytosis; Kostmann's disease. Excludes1 (not coded here): neutropenic splenomegaly (D73.81); transient neonatal neutropenia (P61.5). Use additional code: code for any associated:; fever (R50.81). Code also: , if applicable, mucositis (J34.81, K12.3-, K92.81, N76.81).","officialDefinition":"Congenital agranulocytosis is a billable ICD-10-CM diagnosis code (D70.0). Includes: agranulocytosis; decreased absolute neurophile count (ANC). Inclusion terms: Congenital neutropenia; Infantile genetic agranulocytosis; Kostmann's disease. Excludes1 (not coded here): neutropenic splenomegaly (D73.81); transient neonatal neutropenia (P61.5). Use additional code: code for any associated:; fever (R50.81). Code also: , if applicable, mucositis (J34.81, K12.3-, K92.81, N76.81).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}