{"code":"D81.1","type":"code","title":"Severe combined immunodeficiency [SCID] with low T- and B-cell numbers","codeAlso":[],"includes":["defects in the complement system","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease","sarcoidosis"],"modern_v":"official26","codeFirst":[],"excludes1":["autosomal recessive agammaglobulinemia (Swiss type) (D80.0)","autoimmune disease (systemic) NOS (M35.9)","functional disorders of polymorphonuclear neutrophils (D71-)"],"excludes2":["human immunodeficiency virus [HIV] disease (B20)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"sibling_codes":["D81","D81.0","D81.2","D81.3","D81.4","D81.5","D81.6","D81.7","D81.8","D81.810","D81.818","D81.819","D81.9"],"inclusionTerms":[],"sibling_titles":{"code":"D81.9","title":"Combined immunodeficiency, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Severe combined immunodeficiency [SCID] with low T- and B-cell numbers is a billable ICD-10-CM diagnosis code (D81.1). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Excludes1 (not coded here): autosomal recessive agammaglobulinemia (Swiss type) (D80.0); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","officialDefinition":"Severe combined immunodeficiency [SCID] with low T- and B-cell numbers is a billable ICD-10-CM diagnosis code (D81.1). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Excludes1 (not coded here): autosomal recessive agammaglobulinemia (Swiss type) (D80.0); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":"","noteProvenance":{"autosomal recessive agammaglobulinemia (Swiss type) (D80.0)":"D81","autoimmune disease (systemic) NOS (M35.9)":"D81","functional disorders of polymorphonuclear neutrophils (D71-)":"D81","human immunodeficiency virus [HIV] disease (B20)":"D81","defects in the complement system":"D81","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease":"D81","sarcoidosis":"D81"},"hcc":{"mapped":true,"model":"CMS-HCC V28","paymentYear":"2026","categories":[{"hcc":"114","label":"Common Variable and Combined Immunodeficiencies","family":"Blood","suppresses":[{"hcc":"115","label":"Specified Immunodeficiencies and White Blood Cell Disorders"}]}],"otherModels":[{"model":"CMS-HCC V22","hcc":"47"},{"model":"RxHCC V08","hcc":"99"}]}}