{"code":"D81.31","type":"code","title":"Severe combined immunodeficiency due to adenosine deaminase deficiency","codeAlso":[],"includes":["defects in the complement system","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease","sarcoidosis"],"modern_v":"official26","codeFirst":[],"excludes1":["autosomal recessive agammaglobulinemia (Swiss type) (D80.0)","autoimmune disease (systemic) NOS (M35.9)","functional disorders of polymorphonuclear neutrophils (D71-)"],"excludes2":["human immunodeficiency virus [HIV] disease (B20)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"inclusionTerms":["ADA deficiency with SCID","Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency"],"useAdditionalCode":[],"clinicalDefinition":"Severe combined immunodeficiency due to adenosine deaminase deficiency is a billable ICD-10-CM diagnosis code (D81.31). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: ADA deficiency with SCID; Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency. Excludes1 (not coded here): autosomal recessive agammaglobulinemia (Swiss type) (D80.","officialDefinition":"Severe combined immunodeficiency due to adenosine deaminase deficiency is a billable ICD-10-CM diagnosis code (D81.31). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: ADA deficiency with SCID; Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency. Excludes1 (not coded here): autosomal recessive agammaglobulinemia (Swiss type) (D80.0); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}