{"code":"D81.39","type":"code","title":"Other adenosine deaminase deficiency","codeAlso":[],"includes":["defects in the complement system","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease","sarcoidosis"],"modern_v":"official26","codeFirst":[],"excludes1":["autosomal recessive agammaglobulinemia (Swiss type) (D80.0)","autoimmune disease (systemic) NOS (M35.9)","functional disorders of polymorphonuclear neutrophils (D71-)"],"excludes2":["human immunodeficiency virus [HIV] disease (B20)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"inclusionTerms":["Adenosine deaminase [ADA] deficiency type 1, NOS","Adenosine deaminase [ADA] deficiency type 1, without SCID","Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency","Partial ADA deficiency (type 1)","Partial adenosine deaminase deficiency (type 1)"],"useAdditionalCode":[],"clinicalDefinition":"Other adenosine deaminase deficiency is a billable ICD-10-CM diagnosis code (D81.39). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis.","officialDefinition":"Other adenosine deaminase deficiency is a billable ICD-10-CM diagnosis code (D81.39). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: Adenosine deaminase [ADA] deficiency type 1, NOS; Adenosine deaminase [ADA] deficiency type 1, without SCID; Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency; Partial ADA deficiency (type 1); Partial adenosine deaminase deficiency (type 1). Excludes1 (not coded here): autosomal recessive agammaglobulinemia (Swiss type) (D80.0); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}