{"code":"D81.818","type":"code","title":"Other biotin-dependent carboxylase deficiency","codeAlso":[],"includes":["defects in the complement system","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease","sarcoidosis"],"modern_v":"official26","codeFirst":[],"excludes1":["biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)","autosomal recessive agammaglobulinemia (Swiss type) (D80.0)","autoimmune disease (systemic) NOS (M35.9)","functional disorders of polymorphonuclear neutrophils (D71-)"],"excludes2":["human immunodeficiency virus [HIV] disease (B20)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"inclusionTerms":["Holocarboxylase synthetase deficiency","Other multiple carboxylase deficiency"],"useAdditionalCode":[],"clinicalDefinition":"Other biotin-dependent carboxylase deficiency is a billable ICD-10-CM diagnosis code (D81.818). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: Holocarboxylase synthetase deficiency; Other multiple carboxylase deficiency. Excludes1 (not coded here): biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8); autosomal recessive agammaglobulinemia (Swiss type) (D80.","officialDefinition":"Other biotin-dependent carboxylase deficiency is a billable ICD-10-CM diagnosis code (D81.818). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: Holocarboxylase synthetase deficiency; Other multiple carboxylase deficiency. Excludes1 (not coded here): biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8); autosomal recessive agammaglobulinemia (Swiss type) (D80.0); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}