{"code":"D82.3","type":"code","title":"Immunodeficiency following hereditary defective response to Epstein-Barr virus","codeAlso":[],"includes":["defects in the complement system","immunodeficiency disorders, except human immunodeficiency virus [HIV] disease","sarcoidosis"],"modern_v":"official26","codeFirst":[],"excludes1":["ataxia telangiectasia [Louis-Bar] (G11.3)","autoimmune disease (systemic) NOS (M35.9)","functional disorders of polymorphonuclear neutrophils (D71-)","human immunodeficiency virus [HIV] disease (B20)"],"excludes2":[],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true},"sibling_codes":["D82","D82.0","D82.1","D82.2","D82.4","D82.8","D82.9"],"inclusionTerms":["X-linked lymphoproliferative disease"],"sibling_titles":{"code":"D82.9","title":"Immunodeficiency associated with major defect, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Immunodeficiency following hereditary defective response to Epstein-Barr virus is a billable ICD-10-CM diagnosis code (D82.3). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: X-linked lymphoproliferative disease. Excludes1 (not coded here): ataxia telangiectasia [Louis-Bar] (G11.3); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","officialDefinition":"Immunodeficiency following hereditary defective response to Epstein-Barr virus is a billable ICD-10-CM diagnosis code (D82.3). Includes: defects in the complement system; immunodeficiency disorders, except human immunodeficiency virus [HIV] disease; sarcoidosis. Inclusion terms: X-linked lymphoproliferative disease. Excludes1 (not coded here): ataxia telangiectasia [Louis-Bar] (G11.3); autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71-); human immunodeficiency virus [HIV] disease (B20).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}