{"code":"E71.19","type":"code","title":"Other disorders of branched-chain amino-acid metabolism","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"sibling_codes":["E71","E71.0","E71.1","E71.11","E71.110","E71.111","E71.118","E71.12","E71.120","E71.121","E71.128","E71.2","E71.3","E71.30","E71.31","E71.310","E71.311","E71.312","E71.313","E71.314","E71.318","E71.32","E71.39","E71.4","E71.40","E71.41","E71.42","E71.43","E71.44","E71.440","E71.448","E71.5","E71.50","E71.51","E71.510","E71.511","E71.518","E71.52","E71.520","E71.521","E71.522","E71.528","E71.529","E71.53","E71.54","E71.540","E71.541","E71.542","E71.548"],"inclusionTerms":["Hyperleucine-isoleucinemia","Hypervalinemia"],"sibling_titles":{"code":"E71.548","title":"Other peroxisomal disorders","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Other disorders of branched-chain amino-acid metabolism is a billable ICD-10-CM diagnosis code (E71.19). Inclusion terms: Hyperleucine-isoleucinemia; Hypervalinemia. Excludes1 (not coded here): androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","officialDefinition":"Other disorders of branched-chain amino-acid metabolism is a billable ICD-10-CM diagnosis code (E71.19). Inclusion terms: Hyperleucine-isoleucinemia; Hypervalinemia. Excludes1 (not coded here): androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}