{"code":"E72.4","type":"code","title":"Disorders of ornithine metabolism","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["hereditary choroidal dystrophy (H31.2-)","disorders of:","aromatic amino-acid metabolism (E70.-)","branched-chain amino-acid metabolism (E71.0-E71.2)","fatty-acid metabolism (E71.3)","purine and pyrimidine metabolism (E79.-)","gout (M1A.-, M10.-)","androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"sibling_codes":["E72","E72.0","E72.01","E72.02","E72.03","E72.04","E72.09","E72.1","E72.10","E72.11","E72.12","E72.19","E72.2","E72.20","E72.21","E72.22","E72.23","E72.29","E72.3","E72.5","E72.50","E72.51","E72.52","E72.53","E72.530","E72.538","E72.539","E72.54","E72.540","E72.541","E72.548","E72.549","E72.59","E72.8","E72.81","E72.89","E72.9"],"inclusionTerms":["Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome","Ornithinemia (types I, II)","Ornithine transcarbamylase deficiency"],"sibling_titles":{"code":"E72.9","title":"Disorder of amino-acid metabolism, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Disorders of ornithine metabolism is a billable ICD-10-CM diagnosis code (E72.4). Inclusion terms: Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome; Ornithinemia (types I, II); Ornithine transcarbamylase deficiency. Excludes1 (not coded here): hereditary choroidal dystrophy (H31.2-); disorders of:; aromatic amino-acid metabolism (E70.-); branched-chain amino-acid metabolism (E71.0-E71.2); fatty-acid metabolism (E71.3); purine and pyrimidine metabolism (E79.-); gout (M1A.-, M10.","officialDefinition":"Disorders of ornithine metabolism is a billable ICD-10-CM diagnosis code (E72.4). Inclusion terms: Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome; Ornithinemia (types I, II); Ornithine transcarbamylase deficiency. Excludes1 (not coded here): hereditary choroidal dystrophy (H31.2-); disorders of:; aromatic amino-acid metabolism (E70.-); branched-chain amino-acid metabolism (E71.0-E71.2); fatty-acid metabolism (E71.3); purine and pyrimidine metabolism (E79.-); gout (M1A.-, M10.-); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}