{"code":"E78","type":"category","title":"Disorders of lipoprotein metabolism and other lipidemias","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["sphingolipidosis (E75.0-E75.3)","androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":false,"sibling_codes":["E78.0","E78.01","E78.010","E78.011","E78.019","E78.1","E78.2","E78.3","E78.4","E78.41","E78.49","E78.5","E78.6","E78.7","E78.70","E78.71","E78.72","E78.79","E78.8","E78.81","E78.89","E78.9"],"inclusionTerms":[],"sibling_titles":{"code":"E78.9","title":"Disorder of lipoprotein metabolism, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"is a non-billable ICD-10-CM category code (E78). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","officialDefinition":"Disorders of lipoprotein metabolism and other lipidemias is a non-billable ICD-10-CM category code (E78). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[{"code":"E78.0","title":"Pure hypercholesterolemia","description":"Pure hypercholesterolemia is a non-billable ICD-10-CM category code (E78.0). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":false,"slug":"e78.0-pure-hypercholesterolemia"},{"code":"E78.00","title":"Pure hypercholesterolemia, unspecified","description":"Pure hypercholesterolemia, unspecified is a billable ICD-10-CM diagnosis code (E78.00). Inclusion terms: Fredrickson's hyperlipoproteinemia, type IIa; Hyperbetalipoproteinemia; Low-density-lipoprotein-type [LDL] hyperlipoproteinemia; (Pure) hypercholesterolemia NOS. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.00-pure-hypercholesterolemia-unspecified"},{"code":"E78.01","title":"Familial hypercholesterolemia","description":"Familial hypercholesterolemia is a non-billable ICD-10-CM category code (E78.01). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":false,"slug":"e78.01-familial-hypercholesterolemia"},{"code":"E78.010","title":"Homozygous familial hypercholesterolemia [HoFH]","description":"Homozygous familial hypercholesterolemia [HoFH] is a billable ICD-10-CM diagnosis code (E78.010). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.010-homozygous-familial-hypercholesterolemia-hofh"},{"code":"E78.011","title":"Heterozygous familial hypercholesterolemia [HeFH]","description":"Heterozygous familial hypercholesterolemia [HeFH] is a billable ICD-10-CM diagnosis code (E78.011). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.011-heterozygous-familial-hypercholesterolemia-hefh"},{"code":"E78.019","title":"Familial hypercholesterolemia, unspecified","description":"Familial hypercholesterolemia, unspecified is a billable ICD-10-CM diagnosis code (E78.019). Inclusion terms: Familial hypercholesterolemia NOS. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.019-familial-hypercholesterolemia-unspecified"},{"code":"E78.1","title":"Pure hyperglyceridemia","description":"Pure hyperglyceridemia is a billable ICD-10-CM diagnosis code (E78.1). Inclusion terms: Elevated fasting triglycerides; Endogenous hyperglyceridemia; Fredrickson's hyperlipoproteinemia, type IV; Hyperlipidemia, group B; Hyperprebetalipoproteinemia; Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.1-pure-hyperglyceridemia"},{"code":"E78.2","title":"Mixed hyperlipidemia","description":"Mixed hyperlipidemia is a billable ICD-10-CM diagnosis code (E78.2). Inclusion terms: Broad- or floating-betalipoproteinemia; Combined hyperlipidemia NOS; Elevated cholesterol with elevated triglycerides NEC; Fredrickson's hyperlipoproteinemia, type IIb or III; Hyperbetalipoproteinemia with prebetalipoproteinemia; Hypercholesteremia with endogenous hyperglyceridemia; Hyperlipidemia, group C; Tubo-eruptive xanthoma; Xanthoma tuberosum. Excludes1 (not coded here): cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein] (E75.5); familial combined hyperlipidemia (E78.49); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.2-mixed-hyperlipidemia"},{"code":"E78.3","title":"Hyperchylomicronemia","description":"Hyperchylomicronemia is a billable ICD-10-CM diagnosis code (E78.3). Inclusion terms: Chylomicron retention disease; Fredrickson's hyperlipoproteinemia, type I or V; Hyperlipidemia, group D; Mixed hyperglyceridemia. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.3-hyperchylomicronemia"},{"code":"E78.4","title":"Other hyperlipidemia","description":"Other hyperlipidemia is a non-billable ICD-10-CM category code (E78.4). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":false,"slug":"e78.4-other-hyperlipidemia"},{"code":"E78.41","title":"Elevated Lipoprotein(a)","description":"Elevated Lipoprotein(a) is a billable ICD-10-CM diagnosis code (E78.41). Inclusion terms: Elevated Lp(a). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.41-elevated-lipoproteina"},{"code":"E78.49","title":"Other hyperlipidemia","description":"Other hyperlipidemia is a billable ICD-10-CM diagnosis code (E78.49). Inclusion terms: Familial combined hyperlipidemia. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.49-other-hyperlipidemia"},{"code":"E78.5","title":"Hyperlipidemia, unspecified","description":"Hyperlipidemia, unspecified is a billable ICD-10-CM diagnosis code (E78.5). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.5-hyperlipidemia-unspecified"},{"code":"E78.6","title":"Lipoprotein deficiency","description":"Lipoprotein deficiency is a billable ICD-10-CM diagnosis code (E78.6). Inclusion terms: Abetalipoproteinemia; Depressed HDL cholesterol; High-density lipoprotein deficiency; Hypoalphalipoproteinemia; Hypobetalipoproteinemia (familial); Lecithin cholesterol acyltransferase deficiency; Tangier disease. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.6-lipoprotein-deficiency"},{"code":"E78.7","title":"Disorders of bile acid and cholesterol metabolism","description":"Disorders of bile acid and cholesterol metabolism is a non-billable ICD-10-CM category code (E78.7). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): Niemann-Pick disease type C (E75.242); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":false,"slug":"e78.7-disorders-of-bile-acid-and-cholesterol-metabolism"},{"code":"E78.70","title":"Disorder of bile acid and cholesterol metabolism, unspecified","description":"Disorder of bile acid and cholesterol metabolism, unspecified is a billable ICD-10-CM diagnosis code (E78.70). Excludes1 (not coded here): Niemann-Pick disease type C (E75.242); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.70-disorder-of-bile-acid-and-cholesterol-metabolism-unspecified"},{"code":"E78.71","title":"Barth syndrome","description":"Barth syndrome is a billable ICD-10-CM diagnosis code (E78.71). Excludes1 (not coded here): Niemann-Pick disease type C (E75.242); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.71-barth-syndrome"},{"code":"E78.72","title":"Smith-Lemli-Opitz syndrome","description":"Smith-Lemli-Opitz syndrome is a billable ICD-10-CM diagnosis code (E78.72). Excludes1 (not coded here): Niemann-Pick disease type C (E75.242); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.72-smith-lemli-opitz-syndrome"},{"code":"E78.79","title":"Other disorders of bile acid and cholesterol metabolism","description":"Other disorders of bile acid and cholesterol metabolism is a billable ICD-10-CM diagnosis code (E78.79). Excludes1 (not coded here): Niemann-Pick disease type C (E75.242); sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.79-other-disorders-of-bile-acid-and-cholesterol-metabolism"},{"code":"E78.8","title":"Other disorders of lipoprotein metabolism","description":"Other disorders of lipoprotein metabolism is a non-billable ICD-10-CM category code (E78.8). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":false,"slug":"e78.8-other-disorders-of-lipoprotein-metabolism"},{"code":"E78.81","title":"Lipoid dermatoarthritis","description":"Lipoid dermatoarthritis is a billable ICD-10-CM diagnosis code (E78.81). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.81-lipoid-dermatoarthritis"},{"code":"E78.89","title":"Other lipoprotein metabolism disorders","description":"Other lipoprotein metabolism disorders is a billable ICD-10-CM diagnosis code (E78.89). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.89-other-lipoprotein-metabolism-disorders"},{"code":"E78.9","title":"Disorder of lipoprotein metabolism, unspecified","description":"Disorder of lipoprotein metabolism, unspecified is a billable ICD-10-CM diagnosis code (E78.9). Excludes1 (not coded here): sphingolipidosis (E75.0-E75.3); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"e78.9-disorder-of-lipoprotein-metabolism-unspecified"}],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}