{"code":"E83.821","type":"code","title":"ENPP1 deficiency causing generalized arterial calcification of infancy","codeAlso":[", if applicable, associated conditions such as:","heart failure (I50.-)","other secondary hypertension (I15.8)"],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["dietary mineral deficiency (E58-E61)","parathyroid disorders (E20-E21)","vitamin D deficiency (E55.-)","androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"inclusionTerms":[],"useAdditionalCode":[],"clinicalDefinition":"ENPP1 deficiency causing generalized arterial calcification of infancy is a billable ICD-10-CM diagnosis code (E83.821). Excludes1 (not coded here): dietary mineral deficiency (E58-E61); parathyroid disorders (E20-E21); vitamin D deficiency (E55.-); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1).","officialDefinition":"ENPP1 deficiency causing generalized arterial calcification of infancy is a billable ICD-10-CM diagnosis code (E83.821). Excludes1 (not coded here): dietary mineral deficiency (E58-E61); parathyroid disorders (E20-E21); vitamin D deficiency (E55.-); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-). Code also: , if applicable, associated conditions such as:; heart failure (I50.-); other secondary hypertension (I15.8).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}