{"code":"E85.1","type":"code","title":"Neuropathic heredofamilial amyloidosis","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["Alzheimer's disease (G30.0-)","Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true},"sibling_codes":["E85","E85.0","E85.2","E85.3","E85.4","E85.8","E85.81","E85.82","E85.89","E85.9"],"inclusionTerms":["Amyloid polyneuropathy (Portuguese)","Transthyretin-related (ATTR) familial amyloid polyneuropathy"],"sibling_titles":{"code":"E85.9","title":"Amyloidosis, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Neuropathic heredofamilial amyloidosis is a billable ICD-10-CM diagnosis code (E85.1). Inclusion terms: Amyloid polyneuropathy (Portuguese); Transthyretin-related (ATTR) familial amyloid polyneuropathy. Excludes1 (not coded here): androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Alzheimer's disease (G30.0-); Ehlers-Danlos syndromes (Q79.6-).","officialDefinition":"Neuropathic heredofamilial amyloidosis is a billable ICD-10-CM diagnosis code (E85.1). Inclusion terms: Amyloid polyneuropathy (Portuguese); Transthyretin-related (ATTR) familial amyloid polyneuropathy. Excludes1 (not coded here): androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): Alzheimer's disease (G30.0-); Ehlers-Danlos syndromes (Q79.6-).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}