{"code":"E88.0","type":"code","title":"Disorders of plasma-protein metabolism, not elsewhere classified","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["monoclonal gammopathy (of undetermined significance) (D47.2)","polyclonal hypergammaglobulinemia (D89.0)","Waldenström macroglobulinemia (C88.00)","histiocytosis X (chronic) (C96.6)","androgen insensitivity syndrome (E34.5-)","congenital adrenal hyperplasia (E25.0)","hemolytic anemias attributable to enzyme disorders (D55.-)","Marfan syndrome (Q87.4-)","5-alpha-reductase deficiency (E29.1)"],"excludes2":["disorder of lipoprotein metabolism (E78.-)","Ehlers-Danlos syndromes (Q79.6-)"],"isBillable":false,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":false,"billableFy2027":false},"sibling_codes":["E88.01","E88.02","E88.09"],"inclusionTerms":[],"sibling_titles":{"code":"E88.09","title":"Other disorders of plasma-protein metabolism, not elsewhere classified","isBillable":true},"useAdditionalCode":["codes for associated conditions"],"clinicalDefinition":"Disorders of plasma-protein metabolism, not elsewhere classified is a non-billable ICD-10-CM category code (E88.0). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): monoclonal gammopathy (of undetermined significance) (D47.2); polyclonal hypergammaglobulinemia (D89.0); Waldenström macroglobulinemia (C88.00); histiocytosis X (chronic) (C96.6); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.","officialDefinition":"Disorders of plasma-protein metabolism, not elsewhere classified is a non-billable ICD-10-CM category code (E88.0). A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): monoclonal gammopathy (of undetermined significance) (D47.2); polyclonal hypergammaglobulinemia (D89.0); Waldenström macroglobulinemia (C88.00); histiocytosis X (chronic) (C96.6); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); hemolytic anemias attributable to enzyme disorders (D55.-); Marfan syndrome (Q87.4-); 5-alpha-reductase deficiency (E29.1). Excludes2 (not included here): disorder of lipoprotein metabolism (E78.-); Ehlers-Danlos syndromes (Q79.6-). Use additional code: codes for associated conditions.","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}