{"code":"H49.81","type":"code","title":"Kearns-Sayre syndrome","codeAlso":[", if applicable, other manifestations, such as:","heart block (I45.9)"],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":[],"excludes2":["internal ophthalmoplegia (H52.51-)","internuclear ophthalmoplegia (H51.2-)","progressive supranuclear ophthalmoplegia (G23.1)","nystagmus and other irregular eye movements (H55)"],"isBillable":false,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":false,"billableFy2027":false},"sibling_codes":["H49.811","H49.812","H49.813","H49.819"],"inclusionTerms":["Progressive external ophthalmoplegia with pigmentary retinopathy"],"sibling_titles":{"code":"H49.819","title":"Kearns-Sayre syndrome, unspecified eye","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Kearns-Sayre syndrome is a non-billable ICD-10-CM category code (H49.81). A more specific billable subcode must be selected for claims submission. Inclusion terms: Progressive external ophthalmoplegia with pigmentary retinopathy. Excludes2 (not included here): internal ophthalmoplegia (H52.51-); internuclear ophthalmoplegia (H51.2-); progressive supranuclear ophthalmoplegia (G23.1); nystagmus and other irregular eye movements (H55). Code also: , if applicable, other manifestations, such as:; heart block (I45.9).","officialDefinition":"Kearns-Sayre syndrome is a non-billable ICD-10-CM category code (H49.81). A more specific billable subcode must be selected for claims submission. Inclusion terms: Progressive external ophthalmoplegia with pigmentary retinopathy. Excludes2 (not included here): internal ophthalmoplegia (H52.51-); internuclear ophthalmoplegia (H51.2-); progressive supranuclear ophthalmoplegia (G23.1); nystagmus and other irregular eye movements (H55). Code also: , if applicable, other manifestations, such as:; heart block (I45.9).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":"","hcc":{"mapped":false,"model":"CMS-HCC V28","paymentYear":"2026","categories":[],"otherModels":[]}}