{"code":"M35","type":"category","title":"Other systemic involvement of connective tissue","codeAlso":[],"includes":["autoimmune disease NOS","collagen (vascular) disease NOS","systemic autoimmune disease","systemic collagen (vascular) disease"],"modern_v":"official26","codeFirst":[],"excludes1":["reactive perforating collagenosis (L87.1)","autoimmune disease, single organ or single cell-type -code to relevant condition category"],"excludes2":[],"isBillable":false,"fyEffectivity":{"fy2026":true,"fy2027":true},"sibling_codes":["M35.0","M35.01","M35.02","M35.03","M35.04","M35.05","M35.06","M35.07","M35.08","M35.09","M35.0A","M35.0B","M35.0C","M35.1","M35.2","M35.3","M35.4","M35.5","M35.6","M35.7","M35.8","M35.81","M35.89","M35.9"],"inclusionTerms":[],"sibling_titles":{"code":"M35.9","title":"Systemic involvement of connective tissue, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Other systemic involvement of connective tissue is a non-billable ICD-10-CM category code (M35). A more specific billable subcode must be selected for claims submission. Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","officialDefinition":"Other systemic involvement of connective tissue is a non-billable ICD-10-CM category code (M35). A more specific billable subcode must be selected for claims submission. Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[{"code":"M35.0","title":"Sjögren syndrome","description":"Sjögren syndrome is a non-billable ICD-10-CM category code (M35.0). A more specific billable subcode must be selected for claims submission. Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: Sicca syndrome. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":false,"slug":"m35.0-sjgren-syndrome"},{"code":"M35.00","title":"Sjögren syndrome, unspecified","description":"Sjögren syndrome, unspecified is a billable ICD-10-CM diagnosis code (M35.00). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.00-sjgren-syndrome-unspecified"},{"code":"M35.01","title":"Sjögren syndrome with keratoconjunctivitis","description":"Sjögren syndrome with keratoconjunctivitis is a billable ICD-10-CM diagnosis code (M35.01). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.01-sjgren-syndrome-with-keratoconjunctivitis"},{"code":"M35.02","title":"Sjögren syndrome with lung involvement","description":"Sjögren syndrome with lung involvement is a billable ICD-10-CM diagnosis code (M35.02). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.02-sjgren-syndrome-with-lung-involvement"},{"code":"M35.03","title":"Sjögren syndrome with myopathy","description":"Sjögren syndrome with myopathy is a billable ICD-10-CM diagnosis code (M35.03). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.03-sjgren-syndrome-with-myopathy"},{"code":"M35.04","title":"Sjögren syndrome with tubulo-interstitial nephropathy","description":"Sjögren syndrome with tubulo-interstitial nephropathy is a billable ICD-10-CM diagnosis code (M35.04). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: Renal tubular acidosis in sicca syndrome. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.04-sjgren-syndrome-with-tubulo-interstitial-nephropathy"},{"code":"M35.05","title":"Sjögren syndrome with inflammatory arthritis","description":"Sjögren syndrome with inflammatory arthritis is a billable ICD-10-CM diagnosis code (M35.05). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.05-sjgren-syndrome-with-inflammatory-arthritis"},{"code":"M35.06","title":"Sjögren syndrome with peripheral nervous system involvement","description":"Sjögren syndrome with peripheral nervous system involvement is a billable ICD-10-CM diagnosis code (M35.06). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.06-sjgren-syndrome-with-peripheral-nervous-system-involvement"},{"code":"M35.07","title":"Sjögren syndrome with central nervous system involvement","description":"Sjögren syndrome with central nervous system involvement is a billable ICD-10-CM diagnosis code (M35.07). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.07-sjgren-syndrome-with-central-nervous-system-involvement"},{"code":"M35.08","title":"Sjögren syndrome with gastrointestinal involvement","description":"Sjögren syndrome with gastrointestinal involvement is a billable ICD-10-CM diagnosis code (M35.08). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.08-sjgren-syndrome-with-gastrointestinal-involvement"},{"code":"M35.09","title":"Sjögren syndrome with other organ involvement","description":"Sjögren syndrome with other organ involvement is a billable ICD-10-CM diagnosis code (M35.09). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.09-sjgren-syndrome-with-other-organ-involvement"},{"code":"M35.0A","title":"Sjögren syndrome with glomerular disease","description":"Sjögren syndrome with glomerular disease is a billable ICD-10-CM diagnosis code (M35.0A). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.0a-sjgren-syndrome-with-glomerular-disease"},{"code":"M35.0B","title":"Sjögren syndrome with vasculitis","description":"Sjögren syndrome with vasculitis is a billable ICD-10-CM diagnosis code (M35.0B). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.0b-sjgren-syndrome-with-vasculitis"},{"code":"M35.0C","title":"Sjögren syndrome with dental involvement","description":"Sjögren syndrome with dental involvement is a billable ICD-10-CM diagnosis code (M35.0C). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): dry mouth, unspecified (R68.2); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Use additional code: code to identify associated manifestations.","isBillable":true,"slug":"m35.0c-sjgren-syndrome-with-dental-involvement"},{"code":"M35.1","title":"Other overlap syndromes","description":"Other overlap syndromes is a billable ICD-10-CM diagnosis code (M35.1). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: Mixed connective tissue disease. Excludes1 (not coded here): polyangiitis overlap syndrome (M30.8); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.1-other-overlap-syndromes"},{"code":"M35.2","title":"Behçet's disease","description":"Behçet's disease is a billable ICD-10-CM diagnosis code (M35.2). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.2-behets-disease"},{"code":"M35.3","title":"Polymyalgia rheumatica","description":"Polymyalgia rheumatica is a billable ICD-10-CM diagnosis code (M35.3). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): polymyalgia rheumatica with giant cell arteritis (M31.5); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.3-polymyalgia-rheumatica"},{"code":"M35.4","title":"Diffuse (eosinophilic) fasciitis","description":"Diffuse (eosinophilic) fasciitis is a billable ICD-10-CM diagnosis code (M35.4). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.4-diffuse-eosinophilic-fasciitis"},{"code":"M35.5","title":"Multifocal fibrosclerosis","description":"Multifocal fibrosclerosis is a billable ICD-10-CM diagnosis code (M35.5). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.5-multifocal-fibrosclerosis"},{"code":"M35.6","title":"Relapsing panniculitis [Weber-Christian]","description":"Relapsing panniculitis [Weber-Christian] is a billable ICD-10-CM diagnosis code (M35.6). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): lupus panniculitis (L93.2); panniculitis NOS (M79.3-); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.6-relapsing-panniculitis-weber-christian"},{"code":"M35.7","title":"Hypermobility syndrome","description":"Hypermobility syndrome is a billable ICD-10-CM diagnosis code (M35.7). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: Familial ligamentous laxity. Excludes1 (not coded here): ligamentous laxity, NOS (M24.2-); reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Excludes2 (not included here): Ehlers-Danlos syndromes (Q79.6-).","isBillable":true,"slug":"m35.7-hypermobility-syndrome"},{"code":"M35.8","title":"Other specified systemic involvement of connective tissue","description":"Other specified systemic involvement of connective tissue is a non-billable ICD-10-CM category code (M35.8). A more specific billable subcode must be selected for claims submission. Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":false,"slug":"m35.8-other-specified-systemic-involvement-of-connective-tissue"},{"code":"M35.81","title":"Multisystem inflammatory syndrome","description":"Multisystem inflammatory syndrome is a billable ICD-10-CM diagnosis code (M35.81). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: MIS-A; MIS-C; Multisystem inflammatory syndrome in adults; Multisystem inflammatory syndrome in children; Pediatric inflammatory multisystem syndrome; PIMS. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category. Code first: , if applicable, COVID-19 (U07.1). Use additional code: code, if applicable, for:; exposure to COVID-19 or SARS-CoV-2 infection (Z20.822); personal history of COVID-19 (Z86.16); post COVID-19 condition (U09.9). Code also: any associated complications such as:; acute hepatic failure (K72.0-); acute kidney failure (N17.-); acute myocarditis (I40.-); acute respiratory distress syndrome (J80); cardiac arrhythmia (I47-I49.-); pneumonia due to COVID-19 (J12.82); severe sepsis (R65.2-); viral cardiomyopathy (B33.24); viral pericarditis (B33.23).","isBillable":true,"slug":"m35.81-multisystem-inflammatory-syndrome"},{"code":"M35.89","title":"Other specified systemic involvement of connective tissue","description":"Other specified systemic involvement of connective tissue is a billable ICD-10-CM diagnosis code (M35.89). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.89-other-specified-systemic-involvement-of-connective-tissue"},{"code":"M35.9","title":"Systemic involvement of connective tissue, unspecified","description":"Systemic involvement of connective tissue, unspecified is a billable ICD-10-CM diagnosis code (M35.9). Includes: autoimmune disease NOS; collagen (vascular) disease NOS; systemic autoimmune disease; systemic collagen (vascular) disease. Inclusion terms: Autoimmune disease (systemic) NOS; Collagen (vascular) disease NOS. Excludes1 (not coded here): reactive perforating collagenosis (L87.1); autoimmune disease, single organ or single cell-type -code to relevant condition category.","isBillable":true,"slug":"m35.9-systemic-involvement-of-connective-tissue-unspecified"}],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}