{"code":"Q13.81","type":"code","title":"Rieger anomaly","codeAlso":["any other associated congenital malformations such as cardiac defects"],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":[],"excludes2":["cleft lip and cleft palate (Q35-Q37)","congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)","congenital malformation of larynx (Q31.-)","congenital malformation of lip NEC (Q38.0)","congenital malformation of nose (Q30.-)","congenital malformation of parathyroid gland (Q89.2)","congenital malformation of thyroid gland (Q89.2)"],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"inclusionTerms":["Axenfeld-Rieger syndrome"],"useAdditionalCode":["code for associated glaucoma (H42)"],"clinicalDefinition":"Rieger anomaly is a billable ICD-10-CM diagnosis code (Q13.81). Inclusion terms: Axenfeld-Rieger syndrome. Excludes2 (not included here): cleft lip and cleft palate (Q35-Q37); congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4); congenital malformation of larynx (Q31.-); congenital malformation of lip NEC (Q38.0); congenital malformation of nose (Q30.-); congenital malformation of parathyroid gland (Q89.2); congenital malformation of thyroid gland (Q89.2).","officialDefinition":"Rieger anomaly is a billable ICD-10-CM diagnosis code (Q13.81). Inclusion terms: Axenfeld-Rieger syndrome. Excludes2 (not included here): cleft lip and cleft palate (Q35-Q37); congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4); congenital malformation of larynx (Q31.-); congenital malformation of lip NEC (Q38.0); congenital malformation of nose (Q30.-); congenital malformation of parathyroid gland (Q89.2); congenital malformation of thyroid gland (Q89.2). Use additional code: code for associated glaucoma (H42). Code also: any other associated congenital malformations such as cardiac defects.","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}