{"code":"Q82.2","type":"code","title":"Congenital cutaneous mastocytosis","codeAlso":[],"includes":[],"modern_v":"official26","codeFirst":[],"excludes1":["cutaneous mastocytosis NOS (D47.01)","diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)","malignant mastocytosis (C96.2-)","systemic mastocytosis (D47.02)","urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)","acrodermatitis enteropathica (E83.2)","congenital erythropoietic porphyria (E80.0)","pilonidal cyst or sinus (L05.-)","Sturge-Weber (-Dimitri) syndrome (Q85.89)"],"excludes2":[],"isBillable":true,"fyEffectivity":{"fy2026":true,"fy2027":true,"billableFy2026":true,"billableFy2027":true},"sibling_codes":["Q82","Q82.0","Q82.1","Q82.3","Q82.4","Q82.5","Q82.6","Q82.8","Q82.9"],"inclusionTerms":["Congenital diffuse cutaneous mastocytosis","Congenital maculopapular cutaneous mastocytosis","Congenital urticaria pigmentosa"],"sibling_titles":{"code":"Q82.9","title":"Congenital malformation of skin, unspecified","isBillable":true},"useAdditionalCode":[],"clinicalDefinition":"Congenital cutaneous mastocytosis is a billable ICD-10-CM diagnosis code (Q82.2). Inclusion terms: Congenital diffuse cutaneous mastocytosis; Congenital maculopapular cutaneous mastocytosis; Congenital urticaria pigmentosa. Excludes1 (not coded here): cutaneous mastocytosis NOS (D47.01); diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01); malignant mastocytosis (C96.2-); systemic mastocytosis (D47.","officialDefinition":"Congenital cutaneous mastocytosis is a billable ICD-10-CM diagnosis code (Q82.2). Inclusion terms: Congenital diffuse cutaneous mastocytosis; Congenital maculopapular cutaneous mastocytosis; Congenital urticaria pigmentosa. Excludes1 (not coded here): cutaneous mastocytosis NOS (D47.01); diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01); malignant mastocytosis (C96.2-); systemic mastocytosis (D47.02); urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01); acrodermatitis enteropathica (E83.2); congenital erythropoietic porphyria (E80.0); pilonidal cyst or sinus (L05.-); Sturge-Weber (-Dimitri) syndrome (Q85.89).","seventhCharacterInstructions":[],"workflowProtocols":[],"guidelines":{"whenToUse":[],"whenNotToUse":[],"commonBillingMistakes":[],"codeComparisons":[],"documentationChecklist":[]},"domainLandscape":{"summary":"Primary diagnostic domain and clinical landscape evaluation.","keyCategories":[],"diagnosticContinuum":"Progression continuum from acute presentation to resolution."},"children":[],"hierarchy":[],"relatedCodes":[],"relevantCPTCodes":[],"documentationTips":[],"caseStudies":[],"description":"","overview":""}