ICD-10/E00

E00 ICD 2026 Code: Congenital iodine-deficiency syndrome

E00 is the authoritative medical code for Congenital iodine-deficiency syndrome. This classification is used in medical billing and clinical recording to specify the clinical criteria for congenital iodine-deficiency syndrome (ICD-10-CM E00), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.

Official Registry Overview & Definition

Congenital iodine-deficiency syndrome is a non-billable ICD-10-CM category code E00. A more specific billable subcode must be selected for claims submission. Excludes1 (not coded here): subclinical iodine-deficiency hypothyroidism E02. Use additional code: code F70-F79 to identify associated intellectual disabilities..

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for E00 in the official ICD-10-CM tabular list.

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • subclinical iodine-deficiency hypothyroidism E02

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • code F70-F79 to identify associated intellectual disabilities.

Frequently Asked Questions (FAQ) & Clinical Guidance

Can E00 be billed directly?

No. E00 (Congenital iodine-deficiency syndrome) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.

What can't be coded together with E00?

Per Excludes1 instructions, E00 must not be reported with: subclinical iodine-deficiency hypothyroidism (E02).

Is an additional code needed with E00?

Use additional code(s) to specify: code (F70-F79) to identify associated intellectual disabilities..

Codes in This Family (4)

Official ICD-10-CM classifications in the same code family as E00, with their registry titles.

  • E00.0 — Congenital iodine-deficiency syndrome, neurological type
  • E00.1 — Congenital iodine-deficiency syndrome, myxedematous type
  • E00.2 — Congenital iodine-deficiency syndrome, mixed type
  • E00.9 — Congenital iodine-deficiency syndrome, unspecified

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

ICD Code E01 Iodine-deficiency related thyroid disorders and allied conditions
ICD Code E02 Subclinical iodine-deficiency hypothyroidism
ICD Code E03 Other hypothyroidism
ICD Code E04 Other nontoxic goiter
ICD Code E05 Thyrotoxicosis [hyperthyroidism]
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