E74.09 is the authoritative medical code for Other glycogen storage disease. This classification is used in medical billing and clinical recording to specify the clinical criteria for other glycogen storage disease (ICD-10-CM E74.09), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Other glycogen storage disease is a billable ICD-10-CM diagnosis code E74.09. Inclusion terms: Andersen disease; Glycogen storage disease, types 0, IV, VI-XI; Hers disease; Liver phosphorylase deficiency; Muscle phosphofructokinase deficiency; Tauri disease. Excludes1 (not coded here): diabetes mellitus E08-E13; hypoglycemia NOS E16.2; increased secretion of glucagon E16.3; mucopolysaccharidosis E76.0-E76.3; androgen insensitivity syndrome E34.5-; congenital adrenal hyperplasia E25.0; hemolytic anemias attributable to enzyme disorders D55.-; Marfan syndrome Q87.4-; 5-alpha-reductase deficiency E29.1. Excludes2 (not included here): Ehlers-Danlos syndromes Q79.6-.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for E74.09 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Andersen disease
- Glycogen storage disease, types 0, IV, VI-XI
- Hers disease
- Liver phosphorylase deficiency
- Muscle phosphofructokinase deficiency
- Tauri disease
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- diabetes mellitus E08-E13
- hypoglycemia NOS E16.2
- increased secretion of glucagon E16.3
- mucopolysaccharidosis E76.0-E76.3
- androgen insensitivity syndrome E34.5-
- congenital adrenal hyperplasia E25.0
- hemolytic anemias attributable to enzyme disorders D55.-
- Marfan syndrome Q87.4-
- 5-alpha-reductase deficiency E29.1
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- Ehlers-Danlos syndromes Q79.6-
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with E74.09?
Per Excludes1 instructions, E74.09 must not be reported with: diabetes mellitus (E08-E13); hypoglycemia NOS (E16.2); increased secretion of glucagon (E16.3); mucopolysaccharidosis (E76.0-E76.3).
Can E74.09 be reported alongside related conditions?
Per Excludes2 instructions, E74.09 and the following may both be reported when both are present: Ehlers-Danlos syndromes (Q79.6-).
What conditions are included under E74.09?
Other glycogen storage disease includes: Andersen disease; Glycogen storage disease, types 0, IV, VI-XI; Hers disease; Liver phosphorylase deficiency; Muscle phosphofructokinase deficiency.
Codes in This Family (30)
Official ICD-10-CM classifications in the same code family as E74.09, with their registry titles.
- E74 — Other disorders of carbohydrate metabolism
- E74.0 — Glycogen storage disease
- E74.01 — von Gierke disease
- E74.02 — Pompe disease
- E74.03 — Cori disease
- E74.04 — McArdle disease
- E74.05 — Lysosome-associated membrane protein 2 [LAMP2] deficiency
- E74.1 — Disorders of fructose metabolism
- E74.10 — Disorder of fructose metabolism, unspecified
- E74.11 — Essential fructosuria
- E74.12 — Hereditary fructose intolerance
- E74.19 — Other disorders of fructose metabolism
- E74.2 — Disorders of galactose metabolism
- E74.20 — Disorders of galactose metabolism, unspecified
- E74.21 — Galactosemia
- E74.29 — Other disorders of galactose metabolism
- E74.3 — Other disorders of intestinal carbohydrate absorption
- E74.31 — Sucrase-isomaltase deficiency
- E74.39 — Other disorders of intestinal carbohydrate absorption
- E74.4 — Disorders of pyruvate metabolism and gluconeogenesis
- E74.8 — Other specified disorders of carbohydrate metabolism
- E74.81 — Disorders of glucose transport, not elsewhere classified
- E74.810 — Glucose transporter protein type 1 deficiency
- E74.818 — Other disorders of glucose transport
- E74.819 — Disorders of glucose transport, unspecified
- E74.82 — Disorders of citrate metabolism
- E74.820 — SLC13A5 Citrate Transporter Disorder
- E74.829 — Other disorders of citrate metabolism
- E74.89 — Other specified disorders of carbohydrate metabolism
- E74.9 — Disorder of carbohydrate metabolism, unspecified
Indexed Clinical Terms (23)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Andersen's disease (glycogen storage)
- Deficiency, deficient, glycogen synthetase
- Deficiency, deficient, hepatophosphorylase
- Deficiency, deficient, liver phosphorylase
- Deficiency, deficient, muscle, phosphofructokinase
- Deficiency, deficient, phosphorylase kinase, liver
- Disease, diseased, Andersen's (glycogenosis IV)
- Disease, diseased, glycogen storage, Andersen's
- Disease, diseased, glycogen storage, hepatorenal
- Disease, diseased, glycogen storage, Hers'
- Disease, diseased, glycogen storage, liver and kidney
- Disease, diseased, glycogen storage, muscle phosphofructokinase
- Disease, diseased, glycogen storage, Tauri's
- Disease, diseased, glycogen storage, type 0
- Disease, diseased, glycogen storage, type IV
- Disease, diseased, glycogen storage, type VI-XI
- Disease, diseased, Hers' (glycogenosis VI)
- Disease, diseased, liver (chronic) (organic), glycogen storage
- Disease, diseased, Tauri's
- Disorder (of), metabolism NOS, glycogen storage (hepatorenal)
- Hers' disease
- Pyelonephritis, in (due to), glycogen storage disease
- Tauri's disease
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: