H49.813 is the authoritative medical code for Kearns-Sayre syndrome, bilateral. This classification is used in medical billing and clinical recording to specify the clinical criteria for kearns-sayre syndrome, bilateral (ICD-10-CM H49.813), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Kearns-Sayre syndrome, bilateral is a billable ICD-10-CM diagnosis code H49.813. Excludes2 (not included here): internal ophthalmoplegia H52.51-; internuclear ophthalmoplegia H51.2-; progressive supranuclear ophthalmoplegia G23.1; nystagmus and other irregular eye movements H55. Code also: , if applicable, other manifestations, such as:; heart block I45.9.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for H49.813 in the official ICD-10-CM tabular list.
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- internal ophthalmoplegia H52.51-
- internuclear ophthalmoplegia H51.2-
- progressive supranuclear ophthalmoplegia G23.1
- nystagmus and other irregular eye movements H55
Code Also
Additional codes that may be required to fully describe the encounter.
- , if applicable, other manifestations, such as:
- heart block I45.9
Frequently Asked Questions (FAQ) & Clinical Guidance
Can H49.813 be reported alongside related conditions?
Per Excludes2 instructions, H49.813 and the following may both be reported when both are present: internal ophthalmoplegia (H52.51-); internuclear ophthalmoplegia (H51.2-); progressive supranuclear ophthalmoplegia (G23.1); nystagmus and other irregular eye movements (H55).
Codes in This Family (38)
Official ICD-10-CM classifications in the same code family as H49.813, with their registry titles.
- H49 — Paralytic strabismus
- H49-H52 — Disorders of ocular muscles, binocular movement, accommodation and refraction (H49-H52)
- H49.0 — Third [oculomotor] nerve palsy
- H49.00 — Third [oculomotor] nerve palsy, unspecified eye
- H49.01 — Third [oculomotor] nerve palsy, right eye
- H49.02 — Third [oculomotor] nerve palsy, left eye
- H49.03 — Third [oculomotor] nerve palsy, bilateral
- H49.1 — Fourth [trochlear] nerve palsy
- H49.10 — Fourth [trochlear] nerve palsy, unspecified eye
- H49.11 — Fourth [trochlear] nerve palsy, right eye
- H49.12 — Fourth [trochlear] nerve palsy, left eye
- H49.13 — Fourth [trochlear] nerve palsy, bilateral
- H49.2 — Sixth [abducent] nerve palsy
- H49.20 — Sixth [abducent] nerve palsy, unspecified eye
- H49.21 — Sixth [abducent] nerve palsy, right eye
- H49.22 — Sixth [abducent] nerve palsy, left eye
- H49.23 — Sixth [abducent] nerve palsy, bilateral
- H49.3 — Total (external) ophthalmoplegia
- H49.30 — Total (external) ophthalmoplegia, unspecified eye
- H49.31 — Total (external) ophthalmoplegia, right eye
- H49.32 — Total (external) ophthalmoplegia, left eye
- H49.33 — Total (external) ophthalmoplegia, bilateral
- H49.4 — Progressive external ophthalmoplegia
- H49.40 — Progressive external ophthalmoplegia, unspecified eye
- H49.41 — Progressive external ophthalmoplegia, right eye
- H49.42 — Progressive external ophthalmoplegia, left eye
- H49.43 — Progressive external ophthalmoplegia, bilateral
- H49.8 — Other paralytic strabismus
- H49.81 — Kearns-Sayre syndrome
- H49.811 — Kearns-Sayre syndrome, right eye
- H49.812 — Kearns-Sayre syndrome, left eye
- H49.819 — Kearns-Sayre syndrome, unspecified eye
- H49.88 — Other paralytic strabismus
- H49.881 — Other paralytic strabismus, right eye
- H49.882 — Other paralytic strabismus, left eye
- H49.883 — Other paralytic strabismus, bilateral
- H49.889 — Other paralytic strabismus, unspecified eye
- H49.9 — Unspecified paralytic strabismus
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: