K83.01 is the authoritative medical code for Primary sclerosing cholangitis. This classification is used in medical billing and clinical recording to specify the clinical criteria for primary sclerosing cholangitis (ICD-10-CM K83.01), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Primary sclerosing cholangitis is a billable ICD-10-CM diagnosis code K83.01. Excludes1 (not coded here): cholangitic liver abscess K75.0; cholangitis with choledocholithiasis (K80.3-, K80.4-); postcholecystectomy syndrome K91.5. Excludes2 (not included here): chronic nonsuppurative destructive cholangitis K74.3; primary biliary cholangitis K74.3; primary biliary cirrhosis K74.3; conditions involving the gallbladder K81-K82; conditions involving the cystic duct K81-K82.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for K83.01 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- cholangitic liver abscess K75.0
- cholangitis with choledocholithiasis (K80.3-, K80.4-)
- postcholecystectomy syndrome K91.5
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- chronic nonsuppurative destructive cholangitis K74.3
- primary biliary cholangitis K74.3
- primary biliary cirrhosis K74.3
- conditions involving the gallbladder K81-K82
- conditions involving the cystic duct K81-K82
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with K83.01?
Per official ICD-10-CM Excludes1 instructions, K83.01 must not be reported together with: cholangitic liver abscess (K75.0); cholangitis with choledocholithiasis (K80.3-, K80.4-); postcholecystectomy syndrome (K91.5).
Can K83.01 be reported alongside related conditions?
Per official ICD-10-CM Excludes2 instructions, K83.01 and the following are not considered part of each other and may both be reported when both conditions are present: chronic nonsuppurative destructive cholangitis (K74.3); primary biliary cholangitis (K74.3); primary biliary cirrhosis (K74.3); conditions involving the gallbladder (K81-K82).
Nearest Codes in This Family
Official ICD-10-CM classifications closest to K83.01 in its code family, with their registry titles.
- K83 — Other diseases of biliary tract
- K83.0 — Cholangitis
- K83.09 — Other cholangitis
- K83.1 — Obstruction of bile duct
- K83.2 — Perforation of bile duct
- K83.3 — Fistula of bile duct
- K83.4 — Spasm of sphincter of Oddi
- K83.5 — Biliary cyst
- K83.8 — Other specified diseases of biliary tract
- K83.9 — Disease of biliary tract, unspecified
Indexed Clinical Terms (1)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Cholangitis (ascending) (recurrent) (secondary) (stenosing) (suppurative), primary, sclerosing