ICD-10/Q98.3

Q98.3 ICD 2026 Code: Other male with 46, XX karyotype

Q98.3 is the authoritative medical code for Other male with 46, XX karyotype. This classification is used in medical billing and clinical recording to specify the clinical criteria for other male with 46, xx karyotype (ICD-10-CM Q98.3), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Other male with 46, XX karyotype is a billable ICD-10-CM diagnosis code Q98.3. Excludes2 (not included here): mitochondrial metabolic disorders E88.4-.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q98.3 in the official ICD-10-CM tabular list.

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

  • mitochondrial metabolic disorders E88.4-

Frequently Asked Questions (FAQ) & Clinical Guidance

Can Q98.3 be reported alongside related conditions?

Per official ICD-10-CM Excludes2 instructions, Q98.3 and the following are not considered part of each other and may both be reported when both conditions are present: mitochondrial metabolic disorders (E88.4-).

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q98.3 in its code family, with their registry titles.

  • Q98 — Other sex chromosome abnormalities, male phenotype, not elsewhere classified
  • Q98.0 — Klinefelter syndrome karyotype 47, XXY
  • Q98.1 — Klinefelter syndrome, male with more than two X chromosomes
  • Q98.4 — Klinefelter syndrome, unspecified
  • Q98.5 — Karyotype 47, XYY
  • Q98.6 — Male with structurally abnormal sex chromosome
  • Q98.7 — Male with sex chromosome mosaicism
  • Q98.8 — Other specified sex chromosome abnormalities, male phenotype
  • Q98.9 — Sex chromosome abnormality, male phenotype, unspecified

Indexed Clinical Terms (2)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Karyotype, 46,XX
  • Karyotype, 46,XX, male