ICD-10/C96.21

C96.21 ICD 2026 Code: Aggressive systemic mastocytosis

C96.21 is the authoritative medical code for Aggressive systemic mastocytosis. This classification is used in medical billing and clinical recording to specify the clinical criteria for aggressive systemic mastocytosis (ICD-10-CM C96.21), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Aggressive systemic mastocytosis is a billable ICD-10-CM diagnosis code C96.21. Excludes1 (not coded here): indolent mastocytosis D47.02; mast cell leukemia C94.30; mastocytosis congenital cutaneous Q82.2; personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues Z85.79. Excludes2 (not included here): Kaposi's sarcoma of lymph nodes C46.3; secondary and unspecified neoplasm of lymph nodes C77.-; secondary neoplasm of bone marrow C79.52; secondary neoplasm of spleen C78.89.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for C96.21 in the official ICD-10-CM tabular list.

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • indolent mastocytosis D47.02
  • mast cell leukemia C94.30
  • mastocytosis congenital cutaneous Q82.2
  • personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues Z85.79

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

  • Kaposi's sarcoma of lymph nodes C46.3
  • secondary and unspecified neoplasm of lymph nodes C77.-
  • secondary neoplasm of bone marrow C79.52
  • secondary neoplasm of spleen C78.89

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with C96.21?

Per official ICD-10-CM Excludes1 instructions, C96.21 must not be reported together with: indolent mastocytosis (D47.02); mast cell leukemia (C94.30); mastocytosis (congenital) (cutaneous) (Q82.2); personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79).

Can C96.21 be reported alongside related conditions?

Per official ICD-10-CM Excludes2 instructions, C96.21 and the following are not considered part of each other and may both be reported when both conditions are present: Kaposi's sarcoma of lymph nodes (C46.3); secondary and unspecified neoplasm of lymph nodes (C77.-); secondary neoplasm of bone marrow (C79.52); secondary neoplasm of spleen (C78.89).

Nearest Codes in This Family

Official ICD-10-CM classifications closest to C96.21 in its code family, with their registry titles.

  • C96 — Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue
  • C96.0 — Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
  • C96.2 — Malignant mast cell neoplasm
  • C96.20 — Malignant mast cell neoplasm, unspecified
  • C96.22 — Mast cell sarcoma
  • C96.29 — Other malignant mast cell neoplasm
  • C96.4 — Sarcoma of dendritic cells (accessory cells)
  • C96.5 — Multifocal and unisystemic Langerhans-cell histiocytosis
  • C96.6 — Unifocal Langerhans-cell histiocytosis
  • C96.9 — Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified

View all 12 codes in the C96 family

Indexed Clinical Terms (1)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Mastocytosis, aggressive systemic