ICD-10/D48.11

D48.11 ICD 2026 Code: Desmoid tumor

D48.11 is the authoritative medical code for Desmoid tumor. This classification is used in medical billing and clinical recording to specify the clinical criteria for desmoid tumor (ICD-10-CM D48.11), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.

Official Registry Overview & Definition

Desmoid tumor is a non-billable ICD-10-CM category code D48.11. A more specific billable subcode must be selected for claims submission. Inclusion terms: Aggressive fibromatosis. Excludes1 (not coded here): neoplasm of uncertain behavior of articular cartilage D48.0; neoplasm of uncertain behavior of cartilage of larynx D38.0; neoplasm of uncertain behavior of cartilage of nose D38.5; neoplasm of uncertain behavior of connective tissue of breast D48.6-; neurofibromatosis nonmalignant Q85.0-; neoplasms of unspecified behavior D49.-.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for D48.11 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Aggressive fibromatosis

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • neoplasm of uncertain behavior of articular cartilage D48.0
  • neoplasm of uncertain behavior of cartilage of larynx D38.0
  • neoplasm of uncertain behavior of cartilage of nose D38.5
  • neoplasm of uncertain behavior of connective tissue of breast D48.6-
  • neurofibromatosis nonmalignant Q85.0-
  • neoplasms of unspecified behavior D49.-

Frequently Asked Questions (FAQ) & Clinical Guidance

Can D48.11 be billed directly?

No. D48.11 (Desmoid tumor) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.

What can't be coded together with D48.11?

Per official ICD-10-CM Excludes1 instructions, D48.11 must not be reported together with: neoplasm of uncertain behavior of articular cartilage (D48.0); neoplasm of uncertain behavior of cartilage of larynx (D38.0); neoplasm of uncertain behavior of cartilage of nose (D38.5); neoplasm of uncertain behavior of connective tissue of breast (D48.6-).

What conditions are included under D48.11?

Desmoid tumor includes: Aggressive fibromatosis.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to D48.11 in its code family, with their registry titles.

  • D48 — Neoplasm of uncertain behavior of other and unspecified sites
  • D48.0 — Neoplasm of uncertain behavior of bone and articular cartilage
  • D48.1 — Neoplasm of uncertain behavior of connective and other soft tissue
  • D48.110 — Desmoid tumor of head and neck
  • D48.111 — Desmoid tumor of chest wall
  • D48.112 — Desmoid tumor, intrathoracic
  • D48.113 — Desmoid tumor of abdominal wall
  • D48.114 — Desmoid tumor, intraabdominal
  • D48.115 — Desmoid tumor of upper extremity and shoulder girdle
  • D48.116 — Desmoid tumor of lower extremity and pelvic girdle

View all 24 codes in the D48 family

Neoplasm Table Sites (113)

Anatomical sites from the official ICD-10-CM Table of Neoplasms that map to this code, with the matching behavior column.

  • Neoplasm, neoplastic, abdomen, abdominal, wall, connective tissue — Uncertain Behavior
  • Neoplasm, neoplastic, adipose tissue — Uncertain Behavior
  • Neoplasm, neoplastic, aorta (thoracic) — Uncertain Behavior
  • Neoplasm, neoplastic, aorta (thoracic), abdominal — Uncertain Behavior
  • Neoplasm, neoplastic, aponeurosis — Uncertain Behavior
  • Neoplasm, neoplastic, aponeurosis, palmar — Uncertain Behavior
  • Neoplasm, neoplastic, aponeurosis, plantar — Uncertain Behavior
  • Neoplasm, neoplastic, carotid (artery) — Uncertain Behavior
  • Neoplasm, neoplastic, cartilage NEC (articular) (joint), auricular — Uncertain Behavior
  • Neoplasm, neoplastic, cartilage NEC (articular) (joint), ear (external) — Uncertain Behavior
  • Neoplasm, neoplastic, cartilage NEC (articular) (joint), eyelid — Uncertain Behavior
  • Neoplasm, neoplastic, cartilage NEC (articular) (joint), pinna — Uncertain Behavior
  • Neoplasm, neoplastic, coccygeal, body or glomus — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, abdomen — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, abdominal wall — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, ankle — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, antecubital fossa or space — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, arm — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, auricle (ear) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, axilla — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, back — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, buttock — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, calf — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, cervical region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, cheek — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, chest (wall) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, chin — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, diaphragm — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, ear (external) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, elbow — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, extrarectal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, extremity — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, extremity, lower — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, extremity, upper — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, eyelid — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, face — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, finger — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, flank — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, foot — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, forearm — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, forehead — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, gastric — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, gastrointestinal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, gluteal region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, great vessels NEC — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, groin — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, hand — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, head — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, heel — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, hip — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, hypochondrium — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, iliopsoas muscle — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, infraclavicular region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, inguinal (canal) (region) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, intestinal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, intrathoracic — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, ischiorectal fossa — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, jaw — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, knee — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, leg — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, limb NEC — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, limb NEC, lower — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, limb NEC, upper — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, nates — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, neck — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, orbit — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, para-urethral — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, pararectal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, paravaginal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, pelvis (floor) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, pelvo-abdominal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, perineum — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, perirectal (tissue) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, periurethral (tissue) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, popliteal fossa or space — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, presacral — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, psoas muscle — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, pterygoid fossa — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, rectovaginal septum or wall — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, rectovesical — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, sacrococcygeal region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, scalp — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, scapular region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, shoulder — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, stomach — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, submental — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, supraclavicular region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, temple — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, temporal region — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, thigh — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, thoracic (duct) (wall) — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, thorax — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, thumb — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, toe — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, trunk — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, umbilicus — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, vesicorectal — Uncertain Behavior
  • Neoplasm, neoplastic, connective tissue NEC, wrist — Uncertain Behavior
  • Neoplasm, neoplastic, diaphragm — Uncertain Behavior
  • Neoplasm, neoplastic, ear (external), cartilage — Uncertain Behavior
  • Neoplasm, neoplastic, eyelid (lower) (skin) (upper), cartilage — Uncertain Behavior
  • Neoplasm, neoplastic, fascia, palmar — Uncertain Behavior
  • Neoplasm, neoplastic, fascia, plantar — Uncertain Behavior
  • Neoplasm, neoplastic, fossa (of), pterygoid — Uncertain Behavior
  • Neoplasm, neoplastic, glomus, coccygeal — Uncertain Behavior
  • Neoplasm, neoplastic, great vessels NEC — Uncertain Behavior
  • Neoplasm, neoplastic, lymph, lymphatic channel NEC — Uncertain Behavior
  • Neoplasm, neoplastic, lymph, lymphatic channel NEC, vessel — Uncertain Behavior
  • Neoplasm, neoplastic, pterygoid fossa — Uncertain Behavior
  • Neoplasm, neoplastic, thorax, thoracic (cavity) (organs NEC), duct — Uncertain Behavior
  • Neoplasm, neoplastic, vena cava (abdominal) (inferior) — Uncertain Behavior
  • Neoplasm, neoplastic, vena cava (abdominal) (inferior), superior — Uncertain Behavior