D56.5 is the authoritative medical code for Hemoglobin E-beta thalassemia. This classification is used in medical billing and clinical recording to specify the clinical criteria for hemoglobin e-beta thalassemia (ICD-10-CM D56.5), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Hemoglobin E-beta thalassemia is a billable ICD-10-CM diagnosis code D56.5. Excludes1 (not coded here): beta thalassemia D56.1; beta thalassemia minor D56.3; beta thalassemia trait D56.3; delta-beta thalassemia D56.2; delta-beta thalassemia trait D56.3; hemoglobin E disease D58.2; other hemoglobinopathies D58.2; sickle-cell beta thalassemia D57.4-; sickle-cell thalassemia D57.4-.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for D56.5 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- beta thalassemia D56.1
- beta thalassemia minor D56.3
- beta thalassemia trait D56.3
- delta-beta thalassemia D56.2
- delta-beta thalassemia trait D56.3
- hemoglobin E disease D58.2
- other hemoglobinopathies D58.2
- sickle-cell beta thalassemia D57.4-
- sickle-cell thalassemia D57.4-
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with D56.5?
Per Excludes1 instructions, D56.5 must not be reported with: beta thalassemia (D56.1); beta thalassemia minor (D56.3); beta thalassemia trait (D56.3); delta-beta thalassemia (D56.2).
Codes in This Family (8)
Official ICD-10-CM classifications in the same code family as D56.5, with their registry titles.
- D56 — Thalassemia
- D56.0 — Alpha thalassemia
- D56.1 — Beta thalassemia
- D56.2 — Delta-beta thalassemia
- D56.3 — Thalassemia minor
- D56.4 — Hereditary persistence of fetal hemoglobin [HPFH]
- D56.8 — Other thalassemias
- D56.9 — Thalassemia, unspecified
Indexed Clinical Terms (3)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Disease, diseased, hemoglobin or Hb, E-beta thalassemia
- Hemoglobin, E-beta thalassemia
- Thalassemia (anemia) (disease), hemoglobin, E-beta
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:
ICD Code D59.5
Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]