E88.19 is the authoritative medical code for Other lipodystrophy, not elsewhere classified. This classification is used in medical billing and clinical recording to specify the clinical criteria for other lipodystrophy, not elsewhere classified (ICD-10-CM E88.19), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Other lipodystrophy, not elsewhere classified is a billable ICD-10-CM diagnosis code E88.19. Excludes1 (not coded here): Whipple's disease K90.81; histiocytosis X chronic C96.6; androgen insensitivity syndrome E34.5-; congenital adrenal hyperplasia E25.0; hemolytic anemias attributable to enzyme disorders D55.-; Marfan syndrome Q87.4-; 5-alpha-reductase deficiency E29.1. Excludes2 (not included here): Ehlers-Danlos syndromes Q79.6-. Use additional code: codes for associated conditions.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for E88.19 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- Whipple's disease K90.81
- histiocytosis X chronic C96.6
- androgen insensitivity syndrome E34.5-
- congenital adrenal hyperplasia E25.0
- hemolytic anemias attributable to enzyme disorders D55.-
- Marfan syndrome Q87.4-
- 5-alpha-reductase deficiency E29.1
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- Ehlers-Danlos syndromes Q79.6-
Use Additional Code
Supplementary codes the tabular list directs you to add.
- codes for associated conditions
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with E88.19?
Per Excludes1 instructions, E88.19 must not be reported with: Whipple's disease (K90.81); histiocytosis X (chronic) (C96.6); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0).
Can E88.19 be reported alongside related conditions?
Per Excludes2 instructions, E88.19 and the following may both be reported when both are present: Ehlers-Danlos syndromes (Q79.6-).
Is an additional code needed with E88.19?
Use additional code(s) to specify: codes for associated conditions.
Codes in This Family (29)
Official ICD-10-CM classifications in the same code family as E88.19, with their registry titles.
- E88 — Other and unspecified metabolic disorders
- E88.0 — Disorders of plasma-protein metabolism, not elsewhere classified
- E88.01 — Alpha-1-antitrypsin deficiency
- E88.02 — Plasminogen deficiency
- E88.09 — Other disorders of plasma-protein metabolism, not elsewhere classified
- E88.1 — Lipodystrophy, not elsewhere classified
- E88.10 — Lipodystrophy, unspecified
- E88.11 — Partial lipodystrophy
- E88.12 — Generalized lipodystrophy
- E88.13 — Localized lipodystrophy
- E88.14 — HIV-associated lipodystrophy
- E88.2 — Lipomatosis, not elsewhere classified
- E88.3 — Tumor lysis syndrome
- E88.4 — Mitochondrial metabolism disorders
- E88.40 — Mitochondrial metabolism disorder, unspecified
- E88.41 — MELAS syndrome
- E88.42 — MERRF syndrome
- E88.43 — Disorders of mitochondrial tRNA synthetases
- E88.49 — Other mitochondrial metabolism disorders
- E88.8 — Other specified metabolic disorders
- E88.81 — Metabolic syndrome and other insulin resistance
- E88.810 — Metabolic syndrome
- E88.811 — Insulin resistance syndrome, Type A
- E88.818 — Other insulin resistance
- E88.819 — Insulin resistance, unspecified
- E88.82 — Obesity due to disruption of MC4R pathway
- E88.89 — Other specified metabolic disorders
- E88.9 — Metabolic disorder, unspecified
- E88.A — Wasting disease (syndrome) due to underlying condition
Indexed Clinical Terms (2)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Lipodystrophy, specified type NEC
- Syndrome, Hollander-Simons
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: