ICD-10/I27.29

I27.29 ICD 2026 Code: Other secondary pulmonary hypertension

I27.29 is the authoritative medical code for Other secondary pulmonary hypertension. This classification is used in medical billing and clinical recording to specify the clinical criteria for other secondary pulmonary hypertension (ICD-10-CM I27.29), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Other secondary pulmonary hypertension is a billable ICD-10-CM diagnosis code I27.29. Inclusion terms: Group 5 pulmonary hypertension; Pulmonary hypertension with unclear multifactorial mechanisms; Pulmonary hypertension due to hematologic disorders; Pulmonary hypertension due to metabolic disorders; Pulmonary hypertension due to other systemic disorders. Excludes1 (not coded here): Eisenmenger's syndrome I27.83. Code also: other associated disorders, if known, such as:; chronic myeloid leukemia (C92.10-C92.22); essential thrombocythemia D47.3; Gaucher disease E75.22; hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2); hyperthyroidism E05.-; hypothyroidism E00-E03; polycythemia vera D45; sarcoidosis D86.-; associated underlying condition.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for I27.29 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Group 5 pulmonary hypertension
  • Pulmonary hypertension with unclear multifactorial mechanisms
  • Pulmonary hypertension due to hematologic disorders
  • Pulmonary hypertension due to metabolic disorders
  • Pulmonary hypertension due to other systemic disorders

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • Eisenmenger's syndrome I27.83

Code Also

Additional codes that may be required to fully describe the encounter.

  • other associated disorders, if known, such as:
  • chronic myeloid leukemia (C92.10-C92.22)
  • essential thrombocythemia D47.3
  • Gaucher disease E75.22
  • hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
  • hyperthyroidism E05.-
  • hypothyroidism E00-E03
  • polycythemia vera D45
  • sarcoidosis D86.-
  • associated underlying condition

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with I27.29?

Per Excludes1 instructions, I27.29 must not be reported with: Eisenmenger's syndrome (I27.83).

What conditions are included under I27.29?

Other secondary pulmonary hypertension includes: Group 5 pulmonary hypertension; Pulmonary hypertension with unclear multifactorial mechanisms; Pulmonary hypertension due to hematologic disorders; Pulmonary hypertension due to metabolic disorders; Pulmonary hypertension due to other systemic disorders.

Codes in This Family (20)

Official ICD-10-CM classifications in the same code family as I27.29, with their registry titles.

  • I27 — Other pulmonary heart diseases
  • I27.0 — Primary pulmonary hypertension
  • I27.1 — Kyphoscoliotic heart disease
  • I27.2 — Other secondary pulmonary hypertension
  • I27.20 — Pulmonary hypertension, unspecified
  • I27.21 — Secondary pulmonary arterial hypertension
  • I27.22 — Pulmonary hypertension due to left heart disease
  • I27.23 — Pulmonary hypertension due to lung diseases and hypoxia
  • I27.24 — Chronic thromboembolic pulmonary hypertension
  • I27.8 — Other specified pulmonary heart diseases
  • I27.81 — Cor pulmonale (chronic)
  • I27.82 — Chronic pulmonary embolism
  • I27.83 — Eisenmenger's syndrome
  • I27.84 — Fontan related circulation
  • I27.840 — Fontan-associated liver disease [FALD]
  • I27.841 — Fontan-associated lymphatic dysfunction
  • I27.848 — Other Fontan-associated condition
  • I27.849 — Fontan related circulation, unspecified
  • I27.89 — Other specified pulmonary heart diseases
  • I27.9 — Pulmonary heart disease, unspecified

Indexed Clinical Terms (8)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, due to, hematologic disorders
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, due to, metabolic disorders
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, due to, specified systemic disorders NEC
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, group 5
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, secondary, specified NEC
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, with, cor pulmonale (chronic)
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, with, right heart ventricular strain/failure
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, with, unclear multifactorial mechanisms

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

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