I27.83 is the authoritative medical code for Eisenmenger's syndrome. This classification is used in medical billing and clinical recording to specify the clinical criteria for eisenmenger's syndrome (ICD-10-CM I27.83), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Eisenmenger's syndrome is a billable ICD-10-CM diagnosis code I27.83. Inclusion terms: Eisenmenger's complex; Irreversible Eisenmenger's disease; Pulmonary hypertension with right to left shunt related to congenital heart disease. Code also: underlying heart defect, if known, such as:; atrial septal defect Q21.1-; Eisenmenger's defect Q21.8; patent ductus arteriosus Q25.0; ventricular septal defect Q21.0.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for I27.83 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Eisenmenger's complex
- Irreversible Eisenmenger's disease
- Pulmonary hypertension with right to left shunt related to congenital heart disease
Code Also
Additional codes that may be required to fully describe the encounter.
- underlying heart defect, if known, such as:
- atrial septal defect Q21.1-
- Eisenmenger's defect Q21.8
- patent ductus arteriosus Q25.0
- ventricular septal defect Q21.0
Frequently Asked Questions (FAQ) & Clinical Guidance
What conditions are included under I27.83?
Eisenmenger's syndrome includes: Eisenmenger's complex; (Irreversible) Eisenmenger's disease; Pulmonary hypertension with right to left shunt related to congenital heart disease.
Codes in This Family (20)
Official ICD-10-CM classifications in the same code family as I27.83, with their registry titles.
- I27 — Other pulmonary heart diseases
- I27.0 — Primary pulmonary hypertension
- I27.1 — Kyphoscoliotic heart disease
- I27.2 — Other secondary pulmonary hypertension
- I27.20 — Pulmonary hypertension, unspecified
- I27.21 — Secondary pulmonary arterial hypertension
- I27.22 — Pulmonary hypertension due to left heart disease
- I27.23 — Pulmonary hypertension due to lung diseases and hypoxia
- I27.24 — Chronic thromboembolic pulmonary hypertension
- I27.29 — Other secondary pulmonary hypertension
- I27.8 — Other specified pulmonary heart diseases
- I27.81 — Cor pulmonale (chronic)
- I27.82 — Chronic pulmonary embolism
- I27.84 — Fontan related circulation
- I27.840 — Fontan-associated liver disease [FALD]
- I27.841 — Fontan-associated lymphatic dysfunction
- I27.848 — Other Fontan-associated condition
- I27.849 — Fontan related circulation, unspecified
- I27.89 — Other specified pulmonary heart diseases
- I27.9 — Pulmonary heart disease, unspecified
Indexed Clinical Terms (5)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Complex, Eisenmenger's (ventricular septal defect)
- Disease, diseased, Eisenmenger's (irreversible)
- Eisenmenger's, complex or syndrome
- Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic), pulmonary, with, right to left shunt related to congenital heart disease
- Syndrome, Eisenmenger's
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: