ICD-10/L10.4

L10.4 ICD 2026 Code: Pemphigus erythematosus

L10.4 is the authoritative medical code for Pemphigus erythematosus. This classification is used in medical billing and clinical recording to specify the clinical criteria for pemphigus erythematosus (ICD-10-CM L10.4), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Pemphigus erythematosus is a billable ICD-10-CM diagnosis code L10.4. Inclusion terms: Senear-Usher syndrome. Excludes1 (not coded here): pemphigus neonatorum L01.03; benign familial pemphigus Hailey-Hailey; staphylococcal scalded skin syndrome L00; toxic epidermal necrolysis Lyell.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for L10.4 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Senear-Usher syndrome

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • pemphigus neonatorum L01.03
  • benign familial pemphigus Hailey-Hailey
  • staphylococcal scalded skin syndrome L00
  • toxic epidermal necrolysis Lyell

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with L10.4?

Per Excludes1 instructions, L10.4 must not be reported with: pemphigus neonatorum (L01.03); benign familial pemphigus [Hailey-Hailey] (Q82.8); staphylococcal scalded skin syndrome (L00); toxic epidermal necrolysis [Lyell] (L51.2).

What conditions are included under L10.4?

Pemphigus erythematosus includes: Senear-Usher syndrome.

Codes in This Family (8)

Official ICD-10-CM classifications in the same code family as L10.4, with their registry titles.

  • L10 — Pemphigus
  • L10.0 — Pemphigus vulgaris
  • L10.1 — Pemphigus vegetans
  • L10.2 — Pemphigus foliaceous
  • L10.3 — Brazilian pemphigus [fogo selvagem]
  • L10.5 — Drug-induced pemphigus
  • L10.8 — Other pemphigus
  • L10.9 — Pemphigus, unspecified

Indexed Clinical Terms (3)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Pemphigus, erythematosus
  • Senear-Usher disease or syndrome
  • Usher-Senear disease or syndrome

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

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