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L10.1 ICD-10-CM Code: Pemphigus vegetans

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Coding at a Glance

Tabular directives
4 Excludes1
Risk adjustment
CMS-HCC V28: 1 category · RxHCC V08 category 314

Inpatient Payment Groups (MS-DRG)

Potential MS-DRG participation — not a DRG assignment.

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43, Appendix B.

  • MS-DRG 595 — MAJOR SKIN DISORDERS WITH MCC (MDC 09)
  • MS-DRG 596 — MAJOR SKIN DISORDERS WITHOUT MCC (MDC 09)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Risk Adjustment (CMS-HCC)

Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.

  • HCC 387 — Pemphigus, Pemphigoid, and Other Specified Autoimmune Skin Disorders

Other models: RxHCC V08 HCC 314

Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.

Coding instructions

Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for L10.1 in the official ICD-10-CM tabular list, quoted as published.

Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025

Notes without a marker are published on L10.1 itself; “inherited from” names the category or block whose note applies here.

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Coder workflow for L10.1

MedCoder structured workflow — derived from this code’s own official record

Before you code L10.1

  1. Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with L10.1. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).

    See the official tabular notes

Choose the right path

  1. Does the documentation support a condition named in L10.1’s Excludes1 note?
    Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
    No → Continue.

    ReviewL01.03, L00

Consider L10.1. Then confirm the code is valid for the date of service in the Verify section.

Documentation check

The provider’s diagnostic statement
Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).

Official instructions as workflow

  • Excludes1 — check before selecting L10.1(4 notes)

    Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with L10.1: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.

    CompareL01.03, L00

    See the official tabular notes · Guidelines I.A.12.a

Coding decision scenarios

Pattern scenarios for this code’s structure — decision rules, not clinical cases

Documentation: Both the condition L10.1 describes and a condition named in its Excludes1 note are documented for the same encounter.

Coding question: Can both codes be reported?

Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.

Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).

ReviewL01.03, L00

Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.

Code Overview

Pemphigus vegetans is a billable ICD-10-CM diagnosis code (L10.1).

MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.

Indexed Clinical Terms (3)

Official source data — entries quoted as published, in the Index’s own lookup phrasing

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code. These are alphabetic-index entries shown as the Index writes them — lookup phrasing, not necessarily the wording of a final diagnosis.

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.

Relationships & Classification

MedCoder structured relationships — computed from published CMS and AHRQ datasets

MS-DRG Grouper Relationships (FY2026)

Potential MS-DRG participation — not a DRG assignment.

FY2026 MS-DRG: CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 21 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 2 MS-DRGs: DRG 595 (MDC 09), DRG 596 (MDC 09).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):SKN002 — Other specified inflammatory condition of skin (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

L10.0 — Pemphigus vulgaris, L10.2 — Pemphigus foliaceous, L10.3 — Brazilian pemphigus [fogo selvagem], L10.4 — Pemphigus erythematosus, L10.5 — Drug-induced pemphigus, L10.81 — Paraneoplastic pemphigus, L10.89 — Other pemphigus, L10.9 — Pemphigus, unspecified, L12.0 — Bullous pemphigoid, L12.1 — Cicatricial pemphigoid, L12.8 — Other pemphigoid, L12.9 — Pemphigoid, unspecified, L13.8 — Other specified bullous disorders, L13.9 — Bullous disorder, unspecified, L44.8 — Other specified papulosquamous disorders, L44.9 — Papulosquamous disorder, unspecified, L94.2 — Calcinosis cutis, L94.4 — Gottron's papules, L98.7 — Excessive and redundant skin and subcutaneous tissue, L98.8 — Other specified disorders of the skin and subcutaneous tissue

Same CMS-HCC risk category (V28)

CMS maps these diagnoses to the same Hierarchical Condition Category (Pemphigus, Pemphigoid, and Other Specified Autoimmune Skin Disorders) for risk-adjusted payment.

D86.3 — Sarcoidosis of skin, L10.0 — Pemphigus vulgaris, L10.2 — Pemphigus foliaceous, L10.3 — Brazilian pemphigus [fogo selvagem], L10.4 — Pemphigus erythematosus, L10.81 — Paraneoplastic pemphigus, L10.89 — Other pemphigus, L10.9 — Pemphigus, unspecified, L12.0 — Bullous pemphigoid, L12.1 — Cicatricial pemphigoid, L12.8 — Other pemphigoid, L12.9 — Pemphigoid, unspecified, L88 — Pyoderma gangrenosum

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other specified inflammatory condition of skin).

B65.3 — Cercarial dermatitis, E08.620 — Diabetes mellitus due to underlying condition with diabetic dermatitis, E09.620 — Drug or chemical induced diabetes mellitus with diabetic dermatitis, E10.620 — Type 1 diabetes mellitus with diabetic dermatitis, E11.620 — Type 2 diabetes mellitus with diabetic dermatitis, E13.620 — Other specified diabetes mellitus with diabetic dermatitis, L10.0 — Pemphigus vulgaris, L10.2 — Pemphigus foliaceous, L10.3 — Brazilian pemphigus [fogo selvagem], L10.4 — Pemphigus erythematosus, L10.5 — Drug-induced pemphigus, L10.81 — Paraneoplastic pemphigus, L10.89 — Other pemphigus, L10.9 — Pemphigus, unspecified, L11.0 — Acquired keratosis follicularis, L11.1 — Transient acantholytic dermatosis [Grover], L11.8 — Other specified acantholytic disorders, L11.9 — Acantholytic disorder, unspecified, L12.0 — Bullous pemphigoid, L12.1 — Cicatricial pemphigoid, +145 more

Same Index main term, other category

The ICD-10-CM Index to Diseases and Injuries files this code under the main terms “Dermatitis”, “Pemphigus”; these codes share that main term but sit in a different category of the Tabular List.

H01.134 — Eczematous dermatitis of left upper eyelid (eyelid, eczematous, left, upper), H01.135 — Eczematous dermatitis of left lower eyelid (eyelid, eczematous, left, lower), H01.136 — Eczematous dermatitis of left eye, unspecified eyelid (eyelid, eczematous, left), H01.139 — Eczematous dermatitis of unspecified eye, unspecified eyelid (eyelid, eczematous), H01.8 — Other specified inflammations of eyelid (eyelid, specified NEC), H01.9 — Unspecified inflammation of eyelid (eyelid), I87.2 — Venous insufficiency (chronic) (peripheral) (stasis), L00 — Staphylococcal scalded skin syndrome (Ritter's), L01.03 — Bullous impetigo (neonatorum), L08.0 — Pyoderma (septic), L12.0 — Bullous pemphigoid (herpetiformis, senile), L12.1 — Cicatricial pemphigoid (ocular), L12.2 — Chronic bullous disease of childhood (multiformis, juvenile), L13.0 — Dermatitis herpetiformis (circinatus), L13.1 — Subcorneal pustular dermatitis (pustular, subcorneal), L13.8 — Other specified bullous disorders (bullous, bullosa, specified NEC), L13.9 — Bullous disorder, unspecified (bullous, bullosa), L20.82 — Flexural eczema (flexural NEC), L20.89 — Other atopic dermatitis (atopic, specified NEC), L20.9 — Atopic dermatitis, unspecified (atopic), +99 more

Contextual Map

Every relationship of L10.1 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

Clinical classification (CCSR)

Risk adjustment (CMS-HCC)

  • HCC 387 — Pemphigus, Pemphigoid, and Other Specified Autoimmune Skin Disorders [CMS-HCC]— CMS-HCC V28 · 2026

MS-DRG Grouper

  • CC — Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (CC).”— CMS MS-DRG Definitions Manual (Appendix C) · FY2026
  • DRG 595 — MAJOR SKIN DISORDERS WITH MCC[MS-DRG]: “MAJOR SKIN DISORDERS WITH MCC (MDC 09)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026
  • DRG 596 — MAJOR SKIN DISORDERS WITHOUT MCC[MS-DRG]: “MAJOR SKIN DISORDERS WITHOUT MCC (MDC 09)”— CMS MS-DRG Definitions Manual (Appendix B) · FY2026

MDC crossing

  • MDC 09 — Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast[MDC crossing]: “Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs. 7,376 same-MDC procedures group here; browse them on the MDC page.”— CMS MS-DRG Definitions Manual · FY2026

Index entries

  • Dermatitis (eczematous), vegetans[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Neumann's disease or syndrome[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026
  • Pemphigus, vegetans[Index term]— CMS ICD-10-CM Index to Diseases and Injuries · icd10cm-fy2026

Nearest codes (10)

Change history

  • FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016

Sources for this page

Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.

Code, title, tabular notes and index terms Official source data
CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
Claim edits Official source data
CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
Inpatient payment groups Official source data
CMS MS-DRG Definitions Manual (incl. Appendix B diagnosis index, Appendix C CC/MCC list, Appendix E procedure index) and IPPS Final Rule tables — v43 Release, file and checksum · Publisher’s page
Risk adjustment Official source data
2026 Mid-Year Final ICD-10 Mappings + Model Software (cms.gov/files/zip/2026-midyear-final-icd-10-mappings.zip, 2026-midyear-final-model-software.zip) — CMS-HCC V28, PY2026 mid-year final release Release, file and checksum · Publisher’s page
Change history and date-of-service validity Official source data
CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
Comparisons, relationships and the contextual map MedCoder structured relationship
Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
Summary and FAQ answers MedCoder explanation
Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.

Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates

Cite this page

Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.

MedCoder.ai. "L10.1 — Pemphigus vegetans." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/l10.1-pemphigus-vegetans

Change history

  • FY2016 — October 1, 2015
    In the code set at ICD-10-CM adoption
    Pemphigus vegetans

No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to L10.1 in its code family, with their registry titles.

View all codes in the L10 family