ICD-10/N00.1

N00.1 ICD-10-CM Code: Acute nephritic syndrome with focal and segmental glomerular lesions

N00.1 is the authoritative medical code for Acute nephritic syndrome with focal and segmental glomerular lesions. This classification is used in medical billing and clinical recording to specify the clinical criteria for acute nephritic syndrome with focal and segmental glomerular lesions (ICD-10-CM N00.1), ensuring healthcare documentation aligns with current federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Acute nephritic syndrome with focal and segmental glomerular lesions is a billable ICD-10-CM diagnosis code N00.1. Includes: acute glomerular disease; acute glomerulonephritis; acute nephritis. Inclusion terms: Acute nephritic syndrome with focal and segmental hyalinosis; Acute nephritic syndrome with focal and segmental sclerosis; Acute nephritic syndrome with focal glomerulonephritis. Excludes1 (not coded here): acute tubulo-interstitial nephritis N10; nephritic syndrome NOS N05.-; hypertensive chronic kidney disease I12.-. Code also: any associated kidney failure N17-N19..

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for N00.1 in the official ICD-10-CM tabular list.

Includes

Conditions the official ICD-10-CM tabular list includes under this code.

  • acute glomerular disease
  • acute glomerulonephritis
  • acute nephritis

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Acute nephritic syndrome with focal and segmental hyalinosis
  • Acute nephritic syndrome with focal and segmental sclerosis
  • Acute nephritic syndrome with focal glomerulonephritis

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • acute tubulo-interstitial nephritis N10
  • nephritic syndrome NOS N05.-
  • hypertensive chronic kidney disease I12.-

Code Also

Additional codes that may be required to fully describe the encounter.

  • any associated kidney failure N17-N19.

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with N00.1?

Per official ICD-10-CM Excludes1 instructions, N00.1 must not be reported together with: acute tubulo-interstitial nephritis (N10); nephritic syndrome NOS (N05.-); hypertensive chronic kidney disease (I12.-).

What conditions are included under N00.1?

Acute nephritic syndrome with focal and segmental glomerular lesions includes: Acute nephritic syndrome with focal and segmental hyalinosis; Acute nephritic syndrome with focal and segmental sclerosis; Acute nephritic syndrome with focal glomerulonephritis.

Nearest Codes in This Family

Official ICD-10-CM classifications closest to N00.1 in its code family, with their registry titles.

  • N00 — Acute nephritic syndrome
  • N00.0 — Acute nephritic syndrome with minor glomerular abnormality
  • N00.2 — Acute nephritic syndrome with diffuse membranous glomerulonephritis
  • N00.3 — Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
  • N00.4 — Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
  • N00.5 — Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
  • N00.6 — Acute nephritic syndrome with dense deposit disease
  • N00.7 — Acute nephritic syndrome with diffuse crescentic glomerulonephritis
  • N00.8 — Acute nephritic syndrome with other morphologic changes
  • N00.9 — Acute nephritic syndrome with unspecified morphologic changes

View all 14 codes in the N00 family

Indexed Clinical Terms (1)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), acute, with, focal and segmental glomerular lesions