N00 ICD-10-CM Code: Acute nephritic syndrome
Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.
Coding at a Glance
- Tabular directives
- 3 inclusion terms · 3 Excludes1 · 1 code-also instruction
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for N00 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on N00 itself; “inherited from” names the category or block whose note applies here.
Includes
Conditions the official ICD-10-CM tabular list includes under this code.
- acute glomerular disease
- acute glomerulonephritis
- acute nephritis
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- acute tubulo-interstitial nephritis (N10) Compare N00 vs N10 →
- nephritic syndrome NOS (N05.-) Compare N00 vs N05 →
- hypertensive chronic kidney disease (I12.-) inherited from N00-N08Compare N00 vs I12 →
Coder workflow for N00
MedCoder structured workflow — derived from this code’s own official record
Before you code N00
- N00 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).
ReviewN00.0, N00.1, N00.2, N00.3, N00.4, N00.5, N00.6, N00.7, N00.8, N00.9, N00.A, N00.B
See the relationships section · Guide: How to choose an ICD-10-CM code →
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with N00. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support one of the more specific codes beneath N00?
Yes → Select that code and continue the checks below on its own page.
No → N00 cannot be reported as written; query for the specificity its subcategory needs.ReviewN00.0, N00.1, N00.2, N00.3, N00.4, N00.5, N00.6, N00.7, N00.8, N00.9, N00.A, N00.B
- Does the documentation support a condition named in N00’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.
Consider N00. Then review the Code Also note, and confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- Acuity
- Acute or chronic as documented; when both are documented and separate codes exist, both are reported with the acute code first (Guidelines I.B.8).
Official instructions as workflow
Excludes1 — check before selecting N00(3 notes)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with N00: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
See the official tabular notes · Guidelines I.A.12.a
Code Also — related condition(1 note)
Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.
See the official tabular notes · Guidelines I.A.17
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition N00 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Contextual Map
Every relationship of N00 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run N00 with these 6 related codes in Claim Check
Hierarchy
- N00-N99 — Chapter 14: Diseases of the Genitourinary System (N00-N99) (N00-N99)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00-N08 — Glomerular diseases[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Excludes1
- I12 — Hypertensive chronic kidney disease[Excludes1]: “hypertensive chronic kidney disease (I12.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- N05 — Unspecified nephritic syndrome[Excludes1]: “nephritic syndrome NOS (N05.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- N10 — Acute pyelonephritis[Excludes1]: “acute tubulo-interstitial nephritis (N10)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Code Also
- N17 — Acute kidney failure[Code Also]: “any associated kidney failure (N17-N19).”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- N18 — Chronic kidney disease (CKD)[Code Also]: “any associated kidney failure (N17-N19).”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- N19 — Unspecified kidney failure[Code Also]: “any associated kidney failure (N17-N19).”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Nearest codes (14)
- N00.0 — Acute nephritic syndrome with minor glomerular abnormality[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.1 — Acute nephritic syndrome with focal and segmental glomerular lesions[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.2 — Acute nephritic syndrome with diffuse membranous glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.3 — Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.4 — Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.5 — Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.6 — Acute nephritic syndrome with dense deposit disease[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- N00.7 — Acute nephritic syndrome with diffuse crescentic glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 6 more
Change history
- FY2016 — In the code set at ICD-10-CM adoption [Change history]— CMS release files (code change ledger) · icd10cm-fy2016
Common coding questions
Can N00 be billed directly?
No. N00 (Acute nephritic syndrome) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "N00 — Acute nephritic syndrome." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/n00-acute-nephritic-syndrome
Change history
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionAcute nephritic syndrome
No changes since FY2016 — additions, deletions, description changes and billable-status changes are tracked through FY2027 (effective October 1, 2026), and none are recorded for this code. Note changes are tracked from FY2027 only.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to N00 in its code family, with their registry titles.
- N00.0 — Acute nephritic syndrome with minor glomerular abnormality
- N00.1 — Acute nephritic syndrome with focal and segmental glomerular lesions
- N00.2 — Acute nephritic syndrome with diffuse membranous glomerulonephritis
- N00.3 — Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N00.4 — Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N00.5 — Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N00.6 — Acute nephritic syndrome with dense deposit disease
- N00.7 — Acute nephritic syndrome with diffuse crescentic glomerulonephritis
- N00.8 — Acute nephritic syndrome with other morphologic changes
- N00.9 — Acute nephritic syndrome with unspecified morphologic changes
- N00.A — Acute nephritic syndrome with C3 glomerulonephritis
- N00.B — Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis
- N00.B1 — Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
- N00.B2 — Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)