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N01.A ICD-10-CM Code: Rapidly progressive nephritic syndrome with C3 glomerulonephritis

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0, Appendix B.

  • MS-DRG 698 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC (MDC 11)
  • MS-DRG 699 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC (MDC 11)
  • MS-DRG 700 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC (MDC 11)
  • MS-DRG 791 — PREMATURITY WITH MAJOR PROBLEMS (MDC 15)
  • MS-DRG 793 — FULL TERM NEONATE WITH MAJOR PROBLEMS (MDC 15)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Official Registry Overview & Definition

Rapidly progressive nephritic syndrome with C3 glomerulonephritis is a billable ICD-10-CM diagnosis code (N01.A).

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for N01.A in the official ICD-10-CM tabular list.

Includes

Conditions the official ICD-10-CM tabular list includes under this code.

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Code Also

Additional codes that may be required to fully describe the encounter.

  • any associated kidney failure (N17-N19).

Indexed Clinical Terms (2)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), rapidly progressive, with, C3, glomerulonephritis
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), rapidly progressive, with, C3, glomerulopathy

Frequently Compared Codes

The official Excludes notes on N01.A name these codes. Each comparison page covers when the two can — or must not — be reported together.

Change history

  • FY2021 — 2020-10-01
    Added to the code set
    Rapidly progressive nephritic syndrome with C3 glomerulonephritis
    FY2021 changes

Verify Before Coding

  • MCC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.

Relationships & Classification

Official ICD-10-CM tabular notes on other codes that name N01.A or its code family.

1 Excludes1 notes: N01.5.

Potential MS-DRG Relationships (FY2026)

MCC — Major Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 116 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 5 MS-DRGs: DRG 698 (MDC 11), DRG 699 (MDC 11), DRG 700 (MDC 11), DRG 791 (MDC 15), DRG 793 (MDC 15).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):GEN001 — Nephritis; nephrosis; renal sclerosis (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Contextual Map

Every relationship of N01.A in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

  • N00-N99 — Chapter 14: Diseases of the Genitourinary System (N00-N99) (N00-N99) [Hierarchy]
  • N00-N08 — Glomerular diseases [Hierarchy]

Excludes1

  • N01.6 — Rapidly progressive nephritic syndrome with dense deposit disease [Excludes1]: “Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6)” · check together

Referenced by Excludes1 notes

  • N01.5 — Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis [Excludes1]: “Rapidly progressive nephritic syndrome with C3 glomerulonephritis (N01.A)” · check together

Clinical classification (CCSR)

  • GEN001 — Nephritis; nephrosis; renal sclerosis [CCSR]

Potential MS-DRG

  • MCC — Major Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (MCC).”
  • DRG 698 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC [MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC (MDC 11)”
  • DRG 699 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC [MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC (MDC 11)”
  • DRG 700 — OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC [MS-DRG]: “OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC (MDC 11)”
  • DRG 791 — PREMATURITY WITH MAJOR PROBLEMS [MS-DRG]: “PREMATURITY WITH MAJOR PROBLEMS (MDC 15)”
  • DRG 793 — FULL TERM NEONATE WITH MAJOR PROBLEMS [MS-DRG]: “FULL TERM NEONATE WITH MAJOR PROBLEMS (MDC 15)”

MDC crossing · procedures (3574)

  • MDC 11 — Diseases and Disorders of the Kidney and Urinary Tract [MDC crossing]: “Diseases and Disorders of the Kidney and Urinary Tract — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs.”
  • MDC 15 — Newborns and Other Neonates with Conditions Originating in Perinatal Period [MDC crossing]: “Newborns and Other Neonates with Conditions Originating in Perinatal Period — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs.”
  • 00HE0MZ — Insertion of Neurostimulator Lead into Cranial Nerve, Open Approach [Same-MDC procedure]: “Insertion of Neurostimulator Lead into Cranial Nerve, Open Approach — grouped in MDC 11, the procedure side of this code's crossing.” · check together
  • 00HE3MZ — Insertion of Neurostimulator Lead into Cranial Nerve, Percutaneous Approach [Same-MDC procedure]: “Insertion of Neurostimulator Lead into Cranial Nerve, Percutaneous Approach — grouped in MDC 11, the procedure side of this code's crossing.” · check together
  • 00HE4MZ — Insertion of Neurostimulator Lead into Cranial Nerve, Percutaneous Endoscopic Approach [Same-MDC procedure]: “Insertion of Neurostimulator Lead into Cranial Nerve, Percutaneous Endoscopic Approach — grouped in MDC 11, the procedure side of this code's crossing.” · check together
  • 00HU0MZ — Insertion of Neurostimulator Lead into Spinal Canal, Open Approach [Same-MDC procedure]: “Insertion of Neurostimulator Lead into Spinal Canal, Open Approach — grouped in MDC 11, the procedure side of this code's crossing.” · check together
  • 00HU3MZ — Insertion of Neurostimulator Lead into Spinal Canal, Percutaneous Approach [Same-MDC procedure]: “Insertion of Neurostimulator Lead into Spinal Canal, Percutaneous Approach — grouped in MDC 11, the procedure side of this code's crossing.” · check together
  • and 3569 more

Index entries

  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), rapidly progressive, with, C3, glomerulonephritis[Index term]
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic), rapidly progressive, with, C3, glomerulopathy[Index term]

Nearest codes (11)

  • N01 — Rapidly progressive nephritic syndrome [Sibling]
  • N01.0 — Rapidly progressive nephritic syndrome with minor glomerular abnormality [Sibling]
  • N01.1 — Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions [Sibling]
  • N01.2 — Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis [Sibling]
  • N01.3 — Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis [Sibling]
  • N01.4 — Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis [Sibling]
  • N01.5 — Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis [Sibling]
  • N01.6 — Rapidly progressive nephritic syndrome with dense deposit disease [Sibling]
  • and 3 more

Change history

  • FY2021 — Added to the code set [Change history]

Nearest Codes in This Family

Official ICD-10-CM classifications closest to N01.A in its code family, with their registry titles.

  • N01.0 — Rapidly progressive nephritic syndrome with minor glomerular abnormality
  • N01.1 — Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
  • N01.2 — Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
  • N01.3 — Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
  • N01.4 — Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
  • N01.5 — Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
  • N01.6 — Rapidly progressive nephritic syndrome with dense deposit disease
  • N01.7 — Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
  • N01.8 — Rapidly progressive nephritic syndrome with other morphologic changes
  • N01.9 — Rapidly progressive nephritic syndrome with unspecified morphologic changes

View all codes in the N01 family