N04.0 is the authoritative medical code for Nephrotic syndrome with minor glomerular abnormality. This classification is used in medical billing and clinical recording to specify the clinical criteria for nephrotic syndrome with minor glomerular abnormality (ICD-10-CM N04.0), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Nephrotic syndrome with minor glomerular abnormality is a billable ICD-10-CM diagnosis code N04.0. Includes: congenital nephrotic syndrome; lipoid nephrosis. Inclusion terms: Nephrotic syndrome with minimal change lesion. Excludes1 (not coded here): hypertensive chronic kidney disease I12.-. Code also: any associated kidney failure N17-N19..
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for N04.0 in the official ICD-10-CM tabular list.
Includes
Conditions the official ICD-10-CM tabular list includes under this code.
- congenital nephrotic syndrome
- lipoid nephrosis
Inclusion Terms
Alternative terms the tabular list files under this code.
- Nephrotic syndrome with minimal change lesion
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- hypertensive chronic kidney disease I12.-
Code Also
Additional codes that may be required to fully describe the encounter.
- any associated kidney failure N17-N19.
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with N04.0?
Per Excludes1 instructions, N04.0 must not be reported with: hypertensive chronic kidney disease (I12.-).
What conditions are included under N04.0?
Nephrotic syndrome with minor glomerular abnormality includes: Nephrotic syndrome with minimal change lesion.
Codes in This Family (18)
Official ICD-10-CM classifications in the same code family as N04.0, with their registry titles.
- N04 — Nephrotic syndrome
- N04.1 — Nephrotic syndrome with focal and segmental glomerular lesions
- N04.2 — Nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.20 — Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
- N04.21 — Primary membranous nephropathy with nephrotic syndrome
- N04.22 — Secondary membranous nephropathy with nephrotic syndrome
- N04.29 — Other nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.3 — Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
- N04.4 — Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N04.5 — Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
- N04.6 — Nephrotic syndrome with dense deposit disease
- N04.7 — Nephrotic syndrome with diffuse crescentic glomerulonephritis
- N04.8 — Nephrotic syndrome with other morphologic changes
- N04.9 — Nephrotic syndrome with unspecified morphologic changes
- N04.A — Nephrotic syndrome with C3 glomerulonephritis
- N04.B — Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B1 — Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
- N04.B2 — Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Indexed Clinical Terms (2)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Nephrosis, nephrotic (Epstein's) (syndrome) (congenital), minimal change
- Syndrome, nephrotic (congenital), with, minor glomerular abnormality
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:
ICD Code N00.0
Acute nephritic syndrome with minor glomerular abnormality
ICD Code N01.0
Rapidly progressive nephritic syndrome with minor glomerular abnormality
ICD Code N02.0
Recurrent and persistent hematuria with minor glomerular abnormality
ICD Code N03.0
Chronic nephritic syndrome with minor glomerular abnormality
ICD Code N05.0
Unspecified nephritic syndrome with minor glomerular abnormality
ICD Code N07.0
Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality