N04.2 ICD-10-CM Code: Nephrotic syndrome with diffuse membranous glomerulonephritis
Compare with another codeCheck this code on a claim
Billing Status: NO. This is a non-billable ICD-10-CM code: report a more specific billable code beneath it.
Coding at a Glance
- Tabular directives
- 2 inclusion terms · 1 Excludes1 · 1 code-also instruction
Not billable · FY2027A non-billable heading in the tabular list: report a more specific code beneath it.
What you need to know
Source: CMS/NCHS Official ICD-10-CM tabular notes, quoted. From the CMS/NCHS tabular list for the release in force. A note the category or block publishes applies to this code too; the Instructions section marks which is which.
- Excludes1Never report with this code
- hypertensive chronic kidney disease (I12.-)
- Code alsoMay be needed with this code
- any associated kidney failure (N17-N19).
- IncludesWhat this code covers
- congenital nephrotic syndrome
- lipoid nephrosis
Most relevant related codes MedCoder-derived
Read off the official notes above and this code’s own position in the tabular list. Which to report is a documentation question; Compare shows the two side by side.
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for N04.2 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2027Effective: October 1, 2026
Trace:FY2027 changesChange historyRelease, file and checksum
Notes without a marker are published on N04.2 itself; “inherited from” names the category or block whose note applies here.
Includes
Conditions the official ICD-10-CM tabular list includes under this code.
- congenital nephrotic syndrome
- lipoid nephrosis
Source: inherited from N04
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- hypertensive chronic kidney disease (I12.-) Compare N04.2 vs I12 →
Source: inherited from N00-N08
Coder workflow for N04.2
MedCoder structured workflow — derived from this code’s own official record
Before you code N04.2
- N04.2 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).
ReviewN04.20, N04.21, N04.22, N04.29
See the relationships section · Guide: How to choose an ICD-10-CM code →
- N04.2’s title joins a condition with an associated condition or complication. Confirm each component is documented. Where the classification presumes the link through the “with” convention, only a provider statement that the conditions are unrelated defeats it. A combination code is assigned only when it fully identifies the documented conditions; a required second code for the stage, type or manifestation is still reported when the notes ask for it (Guidelines I.B.9, I.A.15).
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with N04.2. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support one of the more specific codes beneath N04.2?
Yes → Select that code and continue the checks below on its own page.
No → N04.2 cannot be reported as written; query for the specificity its subcategory needs. - Does the documentation support a condition named in N04.2’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.ReviewI12
Consider N04.2. Then review the Code Also note, and confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- The associated condition or complication
- Whether the associated condition the title names is documented; the “with” convention presumes some links, and a provider statement that the conditions are unrelated defeats it (Guidelines I.A.15).
Official instructions as workflow
Excludes1 — check before selecting N04.2(1 note)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with N04.2: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
CompareI12
See the official tabular notes · Guidelines I.A.12.a
Code Also — related condition(1 note)
Coding workflow: Review the related condition when both are documented and the instruction applies. A Code Also note does not fix sequencing; the order follows the circumstances of the encounter.
See the official tabular notes · Guidelines I.A.17
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition N04.2 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
ReviewI12
Documentation: Only one of the components this code’s title joins is documented.
Coding question: Is N04.2 supported?
Path: Review the code for the documented component on its own.
Reason: A combination code is assigned only when it fully identifies the documented conditions; otherwise the documented component takes its own code (Guidelines I.B.9).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Coding context
Guidelines, coding notes, decision aids, relationships (with MS-DRG and CCSR classification), hierarchy, HCC, coverage and the context map: what a coder reaches for after the core. Each section names whether it is official source data, a MedCoder-derived relationship or MedCoder editorial.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder-derived relationships — computed from published CMS and AHRQ datasets
Other codes that name N04.2 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 1 Excludes1 note: Q63 — Other congenital malformations of kidney (via N04.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Clinical classification (AHRQ CCSR):GEN001 — Nephritis; nephrosis; renal sclerosis (default).
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Related Codes
Same clinical category (CCSR)
AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Nephritis; nephrosis; renal sclerosis).
N03.3 — Chronic nephritic syndrome with diffuse mesangial proliferative glomerulonephritis, N03.4 — Chronic nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis, N03.5 — Chronic nephritic syndrome with diffuse mesangiocapillary glomerulonephritis, N03.6 — Chronic nephritic syndrome with dense deposit disease, N03.7 — Chronic nephritic syndrome with diffuse crescentic glomerulonephritis, N03.8 — Chronic nephritic syndrome with other morphologic changes, N03.9 — Chronic nephritic syndrome with unspecified morphologic changes, N03.A — Chronic nephritic syndrome with C3 glomerulonephritis, N04.0 — Nephrotic syndrome with minor glomerular abnormality, N04.1 — Nephrotic syndrome with focal and segmental glomerular lesions, N04.20 — Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified, N04.21 — Primary membranous nephropathy with nephrotic syndrome, N04.22 — Secondary membranous nephropathy with nephrotic syndrome, N04.29 — Other nephrotic syndrome with diffuse membranous glomerulonephritis, N04.3 — Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis, N04.4 — Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis, N04.5 — Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis, N04.6 — Nephrotic syndrome with dense deposit disease, N04.7 — Nephrotic syndrome with diffuse crescentic glomerulonephritis, N04.8 — Nephrotic syndrome with other morphologic changes, +112 more
Contextual Map
Every relationship of N04.2 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run N04.2 with this related code in Claim Check
Hierarchy
- N00-N99 — Chapter 14: Diseases of the Genitourinary System (N00-N99) (N00-N99)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N00-N08 — Glomerular diseases[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
Referenced by Excludes1 notes
- Q63 — Other congenital malformations of kidney[Excludes1](via N04.-): “congenital nephrotic syndrome (N04.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2027
Clinical classification (CCSR)
- GEN001 — Nephritis; nephrosis; renal sclerosis[CCSR]— AHRQ CCSR for ICD-10-CM Diagnoses (HCUP)
Nearest codes (18)
- N04 — Nephrotic syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.0 — Nephrotic syndrome with minor glomerular abnormality[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.1 — Nephrotic syndrome with focal and segmental glomerular lesions[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.20 — Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.21 — Primary membranous nephropathy with nephrotic syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.22 — Secondary membranous nephropathy with nephrotic syndrome[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.29 — Other nephrotic syndrome with diffuse membranous glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- N04.3 — Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2027
- and 10 more
Change history (2)
- FY2024 — Became a non-billable header[Change history]— CMS release files (code change ledger) · icd10cm-fy2024
- and 1 more
Reference
Index terms and tables, published questions and FAQ, every source behind this page with its release and checksum, the date-of-service check and the complete change history.
Common coding questions
MedCoder editorial
Can N04.2 be billed directly?
No. N04.2 (Nephrotic syndrome with diffuse membranous glomerulonephritis) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2027 tabular list, index and tables, effective October 1, 2026 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v44.0 (October 2026) Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder-derived relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder editorial explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Current data releases:ICD-10-CM FY2027 · ICD-10-PCS FY2027 · HCPCS October 2026 · MS-DRG v44 · Medicare Code Editor v44.0 · NCCI PTP Q4 2026 · MUE Q4 2026 · NCD code lists 2026-01 · LCD export September 28, 2026 · All releases and sources
Labels on this page: Official source data · MedCoder-derived relationship · MedCoder editorial explanation. How to read the labels · All data sources and release dates · CMS coding rules
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "N04.2 — Nephrotic syndrome with diffuse membranous glomerulonephritis." ICD-10-CM FY2027. https://medcoder.ai/icd10/code/n04.2-nephrotic-syndrome-with-diffuse-membranous-glomerulonephritis
Change history
- FY2024 — October 1, 2023Became a non-billable headerFY2024 changes
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionNephrotic syndrome with diffuse membranous glomerulonephritis
Nearest Codes in This Family
Official ICD-10-CM classifications closest to N04.2 in its code family, with their registry titles.
- N04 — Nephrotic syndrome
- N04.0 — Nephrotic syndrome with minor glomerular abnormality
- N04.1 — Nephrotic syndrome with focal and segmental glomerular lesions
- N04.20 — Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
- N04.21 — Primary membranous nephropathy with nephrotic syndrome
- N04.22 — Secondary membranous nephropathy with nephrotic syndrome
- N04.29 — Other nephrotic syndrome with diffuse membranous glomerulonephritis
- N04.3 — Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
- N04.4 — Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N04.5 — Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis