P78.81 is the authoritative medical code for Congenital cirrhosis (of liver). This classification is used in medical billing and clinical recording to specify the clinical criteria for congenital cirrhosis (of liver) (ICD-10-CM P78.81), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Congenital cirrhosis (of liver) is a billable ICD-10-CM diagnosis code P78.81. Excludes1 (not coded here): cystic fibrosis E84.0-E84.9; neonatal gastrointestinal hemorrhages P54.0-P54.3.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for P78.81 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- cystic fibrosis E84.0-E84.9
- neonatal gastrointestinal hemorrhages P54.0-P54.3
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with P78.81?
Per Excludes1 instructions, P78.81 must not be reported with: cystic fibrosis (E84.0-E84.9); neonatal gastrointestinal hemorrhages (P54.0-P54.3).
Codes in This Family (11)
Official ICD-10-CM classifications in the same code family as P78.81, with their registry titles.
- P78 — Other perinatal digestive system disorders
- P78.0 — Perinatal intestinal perforation
- P78.1 — Other neonatal peritonitis
- P78.2 — Neonatal hematemesis and melena due to swallowed maternal blood
- P78.3 — Noninfective neonatal diarrhea
- P78.8 — Other specified perinatal digestive system disorders
- P78.82 — Peptic ulcer of newborn
- P78.83 — Newborn esophageal reflux
- P78.84 — Gestational alloimmune liver disease
- P78.89 — Other specified perinatal digestive system disorders
- P78.9 — Perinatal digestive system disorder, unspecified
Indexed Clinical Terms (1)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Cirrhosis, cirrhotic (hepatic) (liver), liver, congenital
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: