Skip to main content

D47.01 vs D89.40

D47.01 (Cutaneous mastocytosis) compared with D89.40 (Mast cell activation, unspecified), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.

Can these codes be reported together?

No — do not report together. D89.40 carries an Excludes1 note covering D47.01: “(non-congenital) cutaneous mastocytosis (D47.01)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Side by side

D47.01Cutaneous mastocytosisD89.40Mast cell activation, unspecified
Billing statusBillableBillable
ClassificationC00-D49 — Neoplasms (C00-D49)D50-D89 — Diseases of the Blood and Blood-forming Organs and Certain Disorders Involving the Immune Mechanism (D50-D89)
DefinitionCutaneous mastocytosis is a billable ICD-10-CM diagnosis code (D47.01).Mast cell activation, unspecified is a billable ICD-10-CM diagnosis code (D89.40).
Includes
Diffuse cutaneous mastocytosis
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis
Mast cell activation disorder, unspecified

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources