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Compare/E71.3 vs E71.42

E71.3 vs E71.42

E71.3 (Disorders of fatty-acid metabolism) compared with E71.42 (Carnitine deficiency due to inborn errors of metabolism), from the official CMS tabular data. Both may be reported when both conditions are documented (Excludes2).

Can these codes be reported together?

Yes, when both are documented. E71.3 carries an Excludes2 note covering E71.42: “carnitine deficiency due to inborn error of metabolism (E71.42)”

Excludes2 marks distinct conditions — both may be reported when both are documented.

Side by side

E71.3Disorders of fatty-acid metabolismE71.42Carnitine deficiency due to inborn errors of metabolism
Billing statusNon-billable header

Report instead: E71.30, E71.310, E71.311, E71.312, E71.313

Billable
ClassificationE00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)
DefinitionDisorders of fatty-acid metabolism is a non-billable ICD-10-CM category code (E71.3).Carnitine deficiency due to inborn errors of metabolism is a billable ICD-10-CM diagnosis code (E71.42).

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources