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Compare/E71.313 vs E72.3

E71.313 vs E72.3

E71.313 (Glutaric aciduria type II) compared with E72.3 (Disorders of lysine and hydroxylysine metabolism), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.

Can these codes be reported together?

No — do not report together. E71.313 carries an Excludes1 note covering E72.3: “glutaric aciduria (type 1) NOS (E72.3)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

No — do not report together. E72.3 carries an Excludes1 note covering E71.313: “glutaric aciduria type II (E71.313)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

No — do not report together. E72.3 carries an Excludes1 note covering E71.313: “fatty-acid metabolism (E71.3)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Side by side

E71.313Glutaric aciduria type IIE72.3Disorders of lysine and hydroxylysine metabolism
Billing statusBillableBillable
ClassificationE00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89)
DefinitionGlutaric aciduria type II is a billable ICD-10-CM diagnosis code (E71.313).Disorders of lysine and hydroxylysine metabolism is a billable ICD-10-CM diagnosis code (E72.3).
Includes
Glutaric aciduria type II A
Glutaric aciduria type II B
Glutaric aciduria type II C
Glutaric aciduria NOS
Glutaric aciduria (type I)
Hydroxylysinemia
Hyperlysinemia

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources