E71.314 vs E71.4
E71.314 (Muscle carnitine palmitoyltransferase deficiency) compared with E71.4 (Disorders of carnitine metabolism), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.
Can these codes be reported together?
No — do not report together. E71.4 carries an Excludes1 note covering E71.314: “Muscle carnitine palmitoyltransferase deficiency (E71.314)”
Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
Side by side
| E71.314Muscle carnitine palmitoyltransferase deficiency | E71.4Disorders of carnitine metabolism | |
|---|---|---|
| Billing status | Billable | Non-billable header |
| Classification | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) |
| Definition | Muscle carnitine palmitoyltransferase deficiency is a billable ICD-10-CM diagnosis code (E71.314). | Disorders of carnitine metabolism is a non-billable ICD-10-CM category code (E71.4). |
Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources