E71.510 vs Q87.8
E71.510 (Zellweger syndrome) compared with Q87.8 (Other specified congenital malformation syndromes, not elsewhere classified), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.
Can these codes be reported together?
No — do not report together. Q87.8 carries an Excludes1 note covering E71.510: “Zellweger syndrome (E71.510)”
Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
Side by side
| E71.510Zellweger syndrome | Q87.8Other specified congenital malformation syndromes, not elsewhere classified | |
|---|---|---|
| Billing status | Billable | Non-billable header |
| Classification | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) | Q00-Q99 — Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99) |
| Definition | Zellweger syndrome is a billable ICD-10-CM diagnosis code (E71.510). | Other specified congenital malformation syndromes, not elsewhere classified is a non-billable ICD-10-CM category code (Q87.8). |
| Use additional code | — | code(s) to identify all associated manifestations |
Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources