E74.09 vs E74.1
E74.09 (Other glycogen storage disease) compared with E74.1 (Disorders of fructose metabolism), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.
Can these codes be reported together?
No — do not report together. E74.1 carries an Excludes1 note covering E74.09: “muscle phosphofructokinase deficiency (E74.09)”
Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
Side by side
| E74.09Other glycogen storage disease | E74.1Disorders of fructose metabolism | |
|---|---|---|
| Billing status | Billable | Non-billable header |
| Classification | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) |
| Definition | Other glycogen storage disease is a billable ICD-10-CM diagnosis code (E74.09). | Disorders of fructose metabolism is a non-billable ICD-10-CM category code (E74.1). |
| Includes | Andersen disease Glycogen storage disease, types 0, IV, VI-XI Hers disease Liver phosphorylase deficiency | — |
Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources