E75 vs E77.1
E75 (Disorders of sphingolipid metabolism and other lipid storage disorders) compared with E77.1 (Defects in glycoprotein degradation), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.
Can these codes be reported together?
No — do not report together. E75 carries an Excludes1 note covering E77.1: “mucolipidosis, types I-III (E77.0-E77.1)”
Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
Side by side
| E75Disorders of sphingolipid metabolism and other lipid storage disorders | E77.1Defects in glycoprotein degradation | |
|---|---|---|
| Billing status | Non-billable header | Billable |
| Classification | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) | E00-E89 — Endocrine, Nutritional and Metabolic Diseases (E00-E89) |
| Definition | Disorders of sphingolipid metabolism and other lipid storage disorders is a non-billable ICD-10-CM category code (E75). | Defects in glycoprotein degradation is a billable ICD-10-CM diagnosis code (E77.1). |
| Includes | — | Aspartylglucosaminuria Fucosidosis Mannosidosis Sialidosis [mucolipidosis I] |
Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources