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Compare/K59.3 vs Q43.1

K59.3 vs Q43.1

K59.3 (Megacolon, not elsewhere classified) compared with Q43.1 (Hirschsprung's disease), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.

Can these codes be reported together?

No — do not report together. K59.3 carries an Excludes1 note covering Q43.1: “congenital megacolon (aganglionic) (Q43.1)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

No — do not report together. K59.3 carries an Excludes1 note covering Q43.1: “megacolon (due to) (in) Hirschsprung's disease (Q43.1)”

Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Side by side

K59.3Megacolon, not elsewhere classifiedQ43.1Hirschsprung's disease
Billing statusNon-billable header

Report instead: K59.31, K59.39

Billable
ClassificationK00-K95 — Diseases of the Digestive System (K00-K95)Q00-Q99 — Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99)
DefinitionMegacolon, not elsewhere classified is a non-billable ICD-10-CM category code (K59.3).Hirschsprung's disease is a billable ICD-10-CM diagnosis code (Q43.1).
Includes
Dilatation of colon
Aganglionosis
Congenital (aganglionic) megacolon
Code first
, if applicable (T51-T65) to identify toxic agent

Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources