Q87.43 vs Q87.A
Q87.43 (Marfan syndrome with skeletal manifestation) compared with Q87.A (Loeys-Dietz syndrome), from the official CMS tabular data. Do not report these codes together: the official tabular list marks them Excludes1.
Can these codes be reported together?
No — do not report together. Q87.A carries an Excludes1 note covering Q87.43: “Marfan syndrome (Q87.40-Q87.43)”
Sole exception: when the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
Side by side
| Q87.43Marfan syndrome with skeletal manifestation | Q87.ALoeys-Dietz syndrome | |
|---|---|---|
| Billing status | Billable | Billable |
| Classification | Q00-Q99 — Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99) | Q00-Q99 — Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99) |
| Definition | Marfan syndrome with skeletal manifestation is a billable ICD-10-CM diagnosis code (Q87.43). | — |
| Use additional code | code(s) to identify all associated manifestations | code(s) to identify all associated manifestations |
Derived from the official CMS ICD-10-CM tabular data (FY2026). Not billing advice; verify sequencing rules for the encounter. All data sources