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Digestive congenital anomalies

CCSR category MAL002 · 62 ICD-10-CM codes

Code Families in This Category

  • Q44 Congenital malformations of gallbladder, bile ducts and liver · 11
  • Q43 Other congenital malformations of intestine · 10
  • Q38 Other congenital malformations of tongue, mouth and pharynx · 9
  • Q39 Congenital malformations of esophagus · 9
  • Q40 Other congenital malformations of upper alimentary tract · 6
  • Q42 Congenital absence, atresia and stenosis of large intestine · 6
  • Q45 Other congenital malformations of digestive system · 6
  • Q41 Congenital absence, atresia and stenosis of small intestine · 5

ICD-10-CM Codes in This Category (62)

  • Q38.0 — Congenital malformations of lips, not elsewhere classified
  • Q38.1 — Ankyloglossia
  • Q38.2 — Macroglossia
  • Q38.3 — Other congenital malformations of tongue
  • Q38.4 — Congenital malformations of salivary glands and ducts
  • Q38.5 — Congenital malformations of palate, not elsewhere classified
  • Q38.6 — Other congenital malformations of mouth
  • Q38.7 — Congenital pharyngeal pouch
  • Q38.8 — Other congenital malformations of pharynx
  • Q39.0 — Atresia of esophagus without fistula
  • Q39.1 — Atresia of esophagus with tracheo-esophageal fistula
  • Q39.2 — Congenital tracheo-esophageal fistula without atresia
  • Q39.3 — Congenital stenosis and stricture of esophagus
  • Q39.4 — Esophageal web
  • Q39.5 — Congenital dilatation of esophagus
  • Q39.6 — Congenital diverticulum of esophagus
  • Q39.8 — Other congenital malformations of esophagus
  • Q39.9 — Congenital malformation of esophagus, unspecified
  • Q40.0 — Congenital hypertrophic pyloric stenosis
  • Q40.1 — Congenital hiatus hernia
  • Q40.2 — Other specified congenital malformations of stomach
  • Q40.3 — Congenital malformation of stomach, unspecified
  • Q40.8 — Other specified congenital malformations of upper alimentary tract
  • Q40.9 — Congenital malformation of upper alimentary tract, unspecified
  • Q41.0 — Congenital absence, atresia and stenosis of duodenum
  • Q41.1 — Congenital absence, atresia and stenosis of jejunum
  • Q41.2 — Congenital absence, atresia and stenosis of ileum
  • Q41.8 — Congenital absence, atresia and stenosis of other specified parts of small intestine
  • Q41.9 — Congenital absence, atresia and stenosis of small intestine, part unspecified
  • Q42.0 — Congenital absence, atresia and stenosis of rectum with fistula
  • Q42.1 — Congenital absence, atresia and stenosis of rectum without fistula
  • Q42.2 — Congenital absence, atresia and stenosis of anus with fistula
  • Q42.3 — Congenital absence, atresia and stenosis of anus without fistula
  • Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine
  • Q42.9 — Congenital absence, atresia and stenosis of large intestine, part unspecified
  • Q43.0 — Meckel's diverticulum (displaced) (hypertrophic)
  • Q43.1 — Hirschsprung's disease
  • Q43.2 — Other congenital functional disorders of colon
  • Q43.3 — Congenital malformations of intestinal fixation
  • Q43.4 — Duplication of intestine
  • Q43.5 — Ectopic anus
  • Q43.6 — Congenital fistula of rectum and anus
  • Q43.7 — Persistent cloaca
  • Q43.8 — Other specified congenital malformations of intestine
  • Q43.9 — Congenital malformation of intestine, unspecified
  • Q44.0 — Agenesis, aplasia and hypoplasia of gallbladder
  • Q44.1 — Other congenital malformations of gallbladder
  • Q44.2 — Atresia of bile ducts
  • Q44.3 — Congenital stenosis and stricture of bile ducts
  • Q44.4 — Choledochal cyst
  • Q44.5 — Other congenital malformations of bile ducts
  • Q44.6 — Cystic disease of liver
  • Q44.7 — Other congenital malformations of liver
  • Q44.70 — Other congenital malformation of liver, unspecified
  • Q44.71 — Alagille syndrome
  • Q44.79 — Other congenital malformations of liver
  • Q45.0 — Agenesis, aplasia and hypoplasia of pancreas
  • Q45.1 — Annular pancreas
  • Q45.2 — Congenital pancreatic cyst
  • Q45.3 — Other congenital malformations of pancreas and pancreatic duct
  • Q45.8 — Other specified congenital malformations of digestive system
  • Q45.9 — Congenital malformation of digestive system, unspecified

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, Rockville, MD. All data sources.