D75.0 is the authoritative medical code for Familial erythrocytosis. This classification is used in medical billing and clinical recording to specify the clinical criteria for familial erythrocytosis (ICD-10-CM D75.0), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Familial erythrocytosis is a billable ICD-10-CM diagnosis code D75.0. Inclusion terms: Benign polycythemia; Familial polycythemia. Excludes1 (not coded here): hereditary ovalocytosis D58.1. Excludes2 (not included here): acute lymphadenitis L04.-; chronic lymphadenitis I88.1; enlarged lymph nodes R59.-; hypergammaglobulinemia NOS D89.2; lymphadenitis NOS I88.9; mesenteric lymphadenitis acute chronic I88.0.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for D75.0 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Benign polycythemia
- Familial polycythemia
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- hereditary ovalocytosis D58.1
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- acute lymphadenitis L04.-
- chronic lymphadenitis I88.1
- enlarged lymph nodes R59.-
- hypergammaglobulinemia NOS D89.2
- lymphadenitis NOS I88.9
- mesenteric lymphadenitis acute chronic I88.0
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with D75.0?
Per official ICD-10-CM Excludes1 instructions, D75.0 must not be reported together with: hereditary ovalocytosis (D58.1).
Can D75.0 be reported alongside related conditions?
Per official ICD-10-CM Excludes2 instructions, D75.0 and the following are not considered part of each other and may both be reported when both conditions are present: acute lymphadenitis (L04.-); chronic lymphadenitis (I88.1); enlarged lymph nodes (R59.-); hypergammaglobulinemia NOS (D89.2).
What conditions are included under D75.0?
Familial erythrocytosis includes: Benign polycythemia; Familial polycythemia.
Nearest Codes in This Family
Official ICD-10-CM classifications closest to D75.0 in its code family, with their registry titles.
- D75 — Other and unspecified diseases of blood and blood-forming organs
- D75.1 — Secondary polycythemia
- D75.8 — Other specified diseases of blood and blood-forming organs
- D75.821 — Non-immune heparin-induced thrombocytopenia
- D75.822 — Immune-mediated heparin-induced thrombocytopenia
- D75.828 — Other heparin-induced thrombocytopenia syndrome
- D75.829 — Heparin-induced thrombocytopenia, unspecified
- D75.838 — Other thrombocytosis
- D75.839 — Thrombocytosis, unspecified
- D75.9 — Disease of blood and blood-forming organs, unspecified
View all 11 codes in the D75 family
Indexed Clinical Terms (3)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Erythrocytosis (megalosplenic) (secondary), familial
- Polycythemia (secondary), benign (familial)
- Polycythemia (secondary), familial (benign)