M33.1 ICD-10-CM Code: Other dermatomyositis
Billing Status: NO. This is a clinician non-billable / parent hierarchy grouping in the ICD-10-CM system.
Coding at a Glance
- Tabular directives
- 5 inclusion terms · 1 Excludes1
Coding instructions
Official Tabular Instructional Notes: the inclusion, exclusion and sequencing notes published for M33.1 in the official ICD-10-CM tabular list, quoted as published.
Source: CMS/CDC — ICD-10-CM Tabular ListRelease: FY2026Effective: October 1, 2025
Notes without a marker are published on M33.1 itself; “inherited from” names the category or block whose note applies here.
Includes
Conditions the official ICD-10-CM tabular list includes under this code.
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Source: inherited from M30-M36
Inclusion Terms
Alternative terms the tabular list files under this code.
- Adult dermatomyositis
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Source: inherited from M30-M36
Coder workflow for M33.1
MedCoder structured workflow — derived from this code’s own official record
Before you code M33.1
- M33.1 is not reportable as written. Select the more specific code beneath it that the documentation supports. Codes are reported to the highest level of specificity the classification provides (Guidelines I.B.2).
ReviewM33.10, M33.11, M33.12, M33.13, M33.19
See the relationships section · Guide: How to choose an ICD-10-CM code →
- “Other” (NEC) means the condition is specified in the record but no dedicated code captures it. Confirm the documented form is not one a sibling code names before settling on M33.1; if the record states no specifics at all, the unspecified sibling applies instead. “Other” codes are for documented conditions the classification gives no specific code; “unspecified” codes are for records lacking the detail (Guidelines I.A.9.a, I.A.9.b).
See the relationships section · Guide: Other vs unspecified (NEC vs NOS) →
- Check the Excludes1 note: if the documentation supports a condition named there, do not simply proceed with M33.1. Excludes1 conditions are not reported together with this code unless the record shows they are unrelated (Guidelines I.A.12.a).
Choose the right path
- Does the documentation support one of the more specific codes beneath M33.1?
Yes → Select that code and continue the checks below on its own page.
No → M33.1 cannot be reported as written; query for the specificity its subcategory needs. - Does the documentation support a condition named in M33.1’s Excludes1 note?
Yes → Do not simply proceed: review the excluded code. Both are reported only when the record shows the two conditions are unrelated.
No → Continue.
Consider M33.1. Then confirm the code is valid for the date of service in the Verify section.
Documentation check
- The provider’s diagnostic statement
- Codes are assigned from the provider’s documented diagnosis, not from clinical criteria, test values or a medication list (Guidelines I.A.19).
- Any detail beyond this code’s title
- What the record states that a more specific sibling code would capture — or its absence, which itself supports the unspecified code.
Official instructions as workflow
Excludes1 — check before selecting M33.1(1 note)
Coding workflow: If the documentation supports a condition named in this note, do not simply proceed with M33.1: the two are not reported together. The one exception is when the record shows the two conditions are unrelated to each other.
See the official tabular notes · Guidelines I.A.12.a
Coding decision scenarios
Pattern scenarios for this code’s structure — decision rules, not clinical cases
Documentation: Both the condition M33.1 describes and a condition named in its Excludes1 note are documented for the same encounter.
Coding question: Can both codes be reported?
Path: Review the Excludes1 note and the excluded code, and look for a provider statement on whether the two conditions are related.
Reason: Excludes1 means the two are not coded together; the exception is when the record shows the conditions are unrelated to each other (Guidelines I.A.12.a).
Every row is derived from this code’s own record — its title, tabular notes, 7th-character family and same-category siblings — with fixed MedCoder wording; nothing is inferred about a patient. The official notes and guideline text are in the sections each row links to, and they control.
Code Overview
MedCoder summary Summary composed by MedCoder from this code's official ICD-10-CM record. The tabular instructional notes themselves appear verbatim below.
Verify Before Coding
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim in Claim Check.
Relationships & Classification
MedCoder structured relationships — computed from published CMS and AHRQ datasets
Other codes that name M33.1 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.
Referenced by 7 Excludes1 notes across 3 chapters: G72 — Other and unspecified myopathies (via M33.-), L94 — Other localized connective tissue disorders (via M33.-), M60 — Myositis (via M33.-), M60-M63 — Disorders of muscles (M60-M63) (via M33.-), M61 — Calcification and ossification of muscle (via M33.-), M62 — Other disorders of muscle (via M33.-), M63 — Disorders of muscle in diseases classified elsewhere (via M33.-).
These codes’ tabular lists mark this diagnosis as mutually exclusive — not reported together unless the conditions are documented as unrelated.
Referenced by 2 Excludes2 notes across 2 chapters: I77 — Other disorders of arteries and arterioles (via M33.-), J82 — Pulmonary eosinophilia, not elsewhere classified (via M33.-).
These codes’ tabular lists name this diagnosis as distinct — both may be reported when both are documented.
Referenced by 1 Code First instruction: J84.170 — Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere (via M33.-).
Each of these codes carries a Code First note naming this condition — when that code is reported, THIS code is sequenced first, ahead of it.
Contextual Map
Every relationship of M33.1 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Run M33.1 with these 10 related codes in Claim Check
Hierarchy
- M00-M99 — Chapter 13: Diseases of the Musculoskeletal System and Connective Tissue (M00-M99) (M00-M99)[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M30-M36 — Systemic connective tissue disorders[Hierarchy]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
Referenced by Excludes1 notes
- G72 — Other and unspecified myopathies[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- L94 — Other localized connective tissue disorders[Excludes1](via M33.-): “systemic connective tissue disorders (M30-M36)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- M60 — Myositis[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- M60-M63 — Disorders of muscles (M60-M63)[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- M61 — Calcification and ossification of muscle[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- M62 — Other disorders of muscle[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- M63 — Disorders of muscle in diseases classified elsewhere[Excludes1](via M33.-): “dermatopolymyositis (M33.-)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Referenced by Excludes2 notes
- I77 — Other disorders of arteries and arterioles[Excludes2](via M33.-): “collagen (vascular) diseases (M30-M36)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
- J82 — Pulmonary eosinophilia, not elsewhere classified[Excludes2](via M33.-): “pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Referenced by Code First instructions
- J84.170 — Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere[Code First](via M33.-): “systemic connective tissue disorders (M30-M36)”— CMS ICD-10-CM tabular instructional notes · icd10cm-fy2026
Nearest codes (23)
- M33 — Dermatopolymyositis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.0 — Juvenile dermatomyositis[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.00 — Juvenile dermatomyositis, organ involvement unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.01 — Juvenile dermatomyositis with respiratory involvement[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.02 — Juvenile dermatomyositis with myopathy[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.03 — Juvenile dermatomyositis without myopathy[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.09 — Juvenile dermatomyositis with other organ involvement[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- M33.10 — Other dermatomyositis, organ involvement unspecified[Sibling]— CMS ICD-10-CM tabular structure · icd10cm-fy2026
- and 15 more
Change history (3)
- FY2018 — Description revised[Change history]— CMS release files (code change ledger) · icd10cm-fy2018
- and 2 more
Common coding questions
Can M33.1 be billed directly?
No. M33.1 (Other dermatomyositis) is a non-billable ICD-10-CM category code. A more specific billable subcode must be selected based on clinical documentation.
Sources for this page
Codes, titles, notes, index terms and mappings on this page are transcribed from the datasets below. Relationships MedCoder computed and text MedCoder wrote are labelled where they appear.
- Code, title, tabular notes and index terms Official source data
- CMS/CDC ICD-10-CM FY2026 tabular list, index and tables, effective October 1, 2025 Release, file and checksum · Publisher’s page
- Claim edits Official source data
- CMS Definitions of Medicare Code Edits — v43.1 (April 2026) Release, file and checksum · Publisher’s page
- Change history and date-of-service validity Official source data
- CMS ICD-10-CM release addenda, ingested release by release into the change ledger Release, file and checksum · Publisher’s page
- Comparisons, relationships and the contextual map MedCoder structured relationship
- Computed by MedCoder from the tabular notes and tables above; every derived relationship is marked as derived where it appears
- Summary and FAQ answers MedCoder explanation
- Written by MedCoder to explain the sources above: drafted with AI assistance, checked by a person against the release files, and labelled as MedCoder text where it appears. Not official text.
Labels on this page: Official source data · MedCoder structured relationship · MedCoder explanation. How to read the labels · All data sources and release dates
Cite this page
Reference this page in a research guide, syllabus or article. The release is included because code content changes each year.
MedCoder.ai. "M33.1 — Other dermatomyositis." ICD-10-CM FY2026. https://medcoder.ai/icd10/code/m33.1-other-dermatomyositis
Change history
- FY2018 — October 1, 2017Description revisedOther dermatopolymyositis → Other dermatomyositisFY2018 changes
- FY2018 — October 1, 2017Short description revisedOther dermatopolymyositis → Other dermatomyositisFY2018 changes
- FY2016 — October 1, 2015In the code set at ICD-10-CM adoptionOther dermatopolymyositis
Nearest Codes in This Family
Official ICD-10-CM classifications closest to M33.1 in its code family, with their registry titles.
- M33.00 — Juvenile dermatomyositis, organ involvement unspecified
- M33.01 — Juvenile dermatomyositis with respiratory involvement
- M33.02 — Juvenile dermatomyositis with myopathy
- M33.03 — Juvenile dermatomyositis without myopathy
- M33.09 — Juvenile dermatomyositis with other organ involvement
- M33.10 — Other dermatomyositis, organ involvement unspecified
- M33.11 — Other dermatomyositis with respiratory involvement
- M33.12 — Other dermatomyositis with myopathy
- M33.13 — Other dermatomyositis without myopathy
- M33.19 — Other dermatomyositis with other organ involvement