ICD-10/Q07.00

Q07.00 ICD 2026 Code: Arnold-Chiari syndrome without spina bifida or hydrocephalus

Q07.00 is the authoritative medical code for Arnold-Chiari syndrome without spina bifida or hydrocephalus. This classification is used in medical billing and clinical recording to specify the clinical criteria for arnold-chiari syndrome without spina bifida or hydrocephalus (ICD-10-CM Q07.00), ensuring healthcare documentation aligns with 2026 federal coding standards.

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Official Registry Overview & Definition

Arnold-Chiari syndrome without spina bifida or hydrocephalus is a billable ICD-10-CM diagnosis code Q07.00. Excludes1 (not coded here): Arnold-Chiari syndrome, type III Q01.-; Arnold-Chiari syndrome, type IV Q04.8. Excludes2 (not included here): congenital central alveolar hypoventilation syndrome G47.35; familial dysautonomia Riley-Day; neurofibromatosis nonmalignant Q85.0-.

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q07.00 in the official ICD-10-CM tabular list.

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • Arnold-Chiari syndrome, type III Q01.-
  • Arnold-Chiari syndrome, type IV Q04.8

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

  • congenital central alveolar hypoventilation syndrome G47.35
  • familial dysautonomia Riley-Day
  • neurofibromatosis nonmalignant Q85.0-

Frequently Asked Questions (FAQ) & Clinical Guidance

What can't be coded together with Q07.00?

Per Excludes1 instructions, Q07.00 must not be reported with: Arnold-Chiari syndrome, type III (Q01.-); Arnold-Chiari syndrome, type IV (Q04.8).

Can Q07.00 be reported alongside related conditions?

Per Excludes2 instructions, Q07.00 and the following may both be reported when both are present: congenital central alveolar hypoventilation syndrome (G47.35); familial dysautonomia [Riley-Day] (G90.1); neurofibromatosis (nonmalignant) (Q85.0-).

Codes in This Family (7)

Official ICD-10-CM classifications in the same code family as Q07.00, with their registry titles.

  • Q07 — Other congenital malformations of nervous system
  • Q07.0 — Arnold-Chiari syndrome
  • Q07.01 — Arnold-Chiari syndrome with spina bifida
  • Q07.02 — Arnold-Chiari syndrome with hydrocephalus
  • Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus
  • Q07.8 — Other specified congenital malformations of nervous system
  • Q07.9 — Congenital malformation of nervous system, unspecified

Indexed Clinical Terms (1)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Arnold-Chiari disease, obstruction or syndrome (type II)

Related Codes & Numerical Sequence (Crawl Map)

Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:

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