Q07.01 ICD-10-CM Code: Arnold-Chiari syndrome with spina bifida
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.
- MS-DRG 091 — OTHER DISORDERS OF NERVOUS SYSTEM WITH MCC (MDC 01)
- MS-DRG 092 — OTHER DISORDERS OF NERVOUS SYSTEM WITH CC (MDC 01)
- MS-DRG 093 — OTHER DISORDERS OF NERVOUS SYSTEM WITHOUT CC/MCC (MDC 01)
- MS-DRG 791 — PREMATURITY WITH MAJOR PROBLEMS (MDC 15)
- MS-DRG 793 — FULL TERM NEONATE WITH MAJOR PROBLEMS (MDC 15)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Risk Adjustment (CMS-HCC)
Payment categories this diagnosis maps to under CMS-HCC V28, payment year 2026.
- HCC 182 — Spinal Cord Disorders/Injuries
Other models: CMS-HCC V22 HCC 72 · RxHCC V08 HCC 155
Risk scores depend on the enrollee's full accepted diagnosis set and segment; a category mapping alone does not determine payment.
Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.
Official Registry Overview & Definition
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q07.01 in the official ICD-10-CM tabular list.
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- Arnold-Chiari syndrome, type III (Q01.-)
- Arnold-Chiari syndrome, type IV (Q04.8)
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- congenital central alveolar hypoventilation syndrome (G47.35)
- familial dysautonomia Riley-Day
- neurofibromatosis (nonmalignant) (Q85.0-)
Nearest Codes in This Family
Official ICD-10-CM classifications closest to Q07.01 in its code family, with their registry titles.
- Q07 — Other congenital malformations of nervous system
- Q07.0 — Arnold-Chiari syndrome
- Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.02 — Arnold-Chiari syndrome with hydrocephalus
- Q07.03 — Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8 — Other specified congenital malformations of nervous system
- Q07.9 — Congenital malformation of nervous system, unspecified
Indexed Clinical Terms (3)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Arnold-Chiari disease, obstruction or syndrome (type II), with, spina bifida
- Malformation (congenital), Chiari, Type II
- Syndrome, Dandy-Walker, with spina bifida