Q26.8 is the authoritative medical code for Code. This classification is used in medical billing and clinical recording to specify the clinical criteria for code (ICD-10-CM Q26.8), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Other congenital malformations of great veins is a billable ICD-10-CM diagnosis code Q26.8. Inclusion terms: Absence of vena cava inferior superior; Azygos continuation of inferior vena cava; Persistent left posterior cardinal vein; Scimitar syndrome.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for Q26.8 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Absence of vena cava inferior superior
- Azygos continuation of inferior vena cava
- Persistent left posterior cardinal vein
- Scimitar syndrome
Frequently Asked Questions (FAQ) & Clinical Guidance
What conditions are included under Q26.8?
Code includes: Absence of vena cava (inferior) (superior); Azygos continuation of inferior vena cava; Persistent left posterior cardinal vein; Scimitar syndrome.
Codes in This Family (9)
Official ICD-10-CM classifications in the same code family as Q26.8, with their registry titles.
- Q26 — Congenital malformations of great veins
- Q26.0 — Congenital stenosis of vena cava
- Q26.1 — Persistent left superior vena cava
- Q26.2 — Total anomalous pulmonary venous connection
- Q26.3 — Partial anomalous pulmonary venous connection
- Q26.4 — Anomalous pulmonary venous connection, unspecified
- Q26.5 — Anomalous portal venous connection
- Q26.6 — Portal vein-hepatic artery fistula
- Q26.9 — Congenital malformation of great vein, unspecified
Indexed Clinical Terms (19)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Absence (of) (organ or part) (complete or partial), superior vena cava, congenital
- Absence (of) (organ or part) (complete or partial), veincongenital NEC (peripheral), great
- Absence (of) (organ or part) (complete or partial), vena cava, congenital (inferior) (superior)
- Agenesis, vein (s) (peripheral), great NEC
- Agenesis, vena cava (inferior) (superior)
- Anomaly, anomalous (congenital) (unspecified type), vein (s) (peripheral), great, specified NEC
- Anomaly, anomalous (congenital) (unspecified type), venous return
- Atresia, atretic, vein NEC, great
- Atresia, atretic, vena cava (inferior) (superior)
- Azygos, continuation inferior vena cava
- Hypoplasia, hypoplastic, vein (s) (peripheral), great
- Hypoplasia, hypoplastic, vena cava (inferior) (superior)
- Malformation (congenital), great, vein, specified type NEC
- Malposition, congenital, vein (s) (peripheral), great
- Malposition, congenital, vena cava (inferior) (superior)
- Persistence, persistent (congenital), left, posterior cardinal vein
- Persistence, persistent (congenital), sinus, venosus with imperfect incorporation in right auricle
- Scimitar syndrome
- Syndrome, scimitar
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures:
ICD Code Q23.8
Other congenital malformations of aortic and mitral valves
ICD Code Q27.8
Other specified congenital malformations of peripheral vascular system
ICD Code Q28.8
Other specified congenital malformations of circulatory system